| Title | [Sjögren's syndrome with multiple bullae and pulmonary nodular amyloidosis] | | Author(s) | Teruuchi S, Bando M, Hironaka M, Ohno S, Sugiyama Y | | Institution | Department of Pulmonary Medicine, Jichi Medical School, 3311-1 Yakushiji Minami, Kawachi-machi, Kawachi-gun, Tochigi, Japan. | | Source | Nihon Kokyuki Gakkai Zasshi 2000 Dec; 38(12):918-22. | | MeSH | Amyloidosis
Antiphospholipid Syndrome
Blister
Bronchiolitis
Diagnosis, Differential
English Abstract
Female
Humans
Lung Diseases
Middle Aged
Prednisolone
Sjogren's Syndrome
| | Abstract | We report a case of Sjögren's syndrome with pulmonary involvement diagnosed by open lung biopsy. The patient was a 62-year-old woman with antiphospholipid antibody syndrome. Her chest radiograph and CT scan showed multiple bullae diffusely scattered throughout the lung. The open lung biopsy specimens revealed marked inflammatory mononuclear cell infiltration and nodular amyloid deposits in the bronchiolar walls. The mechanism of bulla formation appeared to be the check valve mechanism caused by the narrowing of the airway by the bronchiolitis. The patient was treated with oral corticosteroids, and her symptoms and laboratory findings became stable. | | Language | jpn | | Pub Type(s) | Case Reports
Journal Article
| | PubMed ID | 11244728 |
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