| Title | The association of cleidocranial dysostosis with hearing loss. |
| Author(s) | Hawkins HB, Shapiro R, Petrillo CJ |
| Source | Am J Roentgenol Radium Ther Nucl Med 1975 Dec; 125(4):944-7. |
| MeSH | Adult
Cleidocranial Dysplasia
Ear, Middle
Female
Hearing Disorders
Humans
Male
Pedigree
|
| Abstract | Three new cases of cleidocranial dysostosis with hearing loss are reported in this paper. The significant points concerning this association are: (1) the hearing deficit is predominantly a middle ear conduction problem secondary to structural abnormalities of the ossicles; (2) there is sometimes a small bone conduction deficit indicating either a cochlear or an eighth nerve problem; (3) the middle ear hearing loss was corrected surgically in one reported case; (4) there is dense sclerosis of the temporal bone which makes a middle ear operation technically difficult; and (5) hearing loss with cleidocranial dysostosis may be more common than the number of cases in the literature suggests. |
| Language | eng |
| Pub Type(s) | Case Reports
Journal Article
|
| PubMed ID | 1211523 |
