Sfaxi M, Bouzouita A, Bouasker I, Kourda N, Ben Slama MR, Ben Jilani Baltaji S, Chebil M
[Primary bilateral adrenal T-cell lymphoma. A case report rarer than B-cell lymphoma.] [JOURNAL ARTICLE]
Ann Endocrinol (Paris) 2008 Apr 30.
Primary adrenal lymphoma is a rare condition. Only 70 cases were described in the literature. Adrenal lymphoma is often bilateral and in most of the cases of B-cell type. T-cell lymphoma is exceptional. The prognosis is bad and patient can die early because of acute adrenal insufficiency. We report a case of a 70-year-old man who was admitted for acute adrenal insufficiency due to primary bilateral adrenal T-cell lymphoma. He had corticotherapy and surgical exploration for intra-abdominal sepsis. He died because of multivisceral deficiency. Clinical features and imaging are not specific. (18)F-FDG PET Scan is an excellent mean to detect malignant tumor of adrenal gland. Percutaneous needle biopsy is useful to determine histology. The standard treatment is chemotherapy.
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