Haruyama T, Furukawa M, Matsumoto F, Kawano K, Ikeda K
Laryngeal stenosis in epidermolysis bullosa dystrophica. [JOURNAL ARTICLE]
Auris Nasus Larynx 2008 May 12.
Epidermolysis bullosa dystrophica is a rare hereditary skin disease of infancy in which minor trauma causes blister formation. We report a rare case of epidermolysis bullosa dystrophica (recessive) with a stenosis of the larynx due to epiglottic deformity. We performed a tracheotomy, and we detained a trachea aperture in the long term this time. In a characteristic of a disease though stimulation to the trachea causes the erosion on a trachea mucous membrane, postoperative course was uneventful and we are going to observe it in future.
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