| Title | Plastic bronchitis as an unusual cause of mucus plugging in cystic fibrosis. | | Author(s) | Mateos-Corral D, Cutz E, Solomon M, Ratjen F | | Institution | Division of Respiratory Medicine, Hospital for Sick Children, Toronto, Canada. | | Source | Pediatr Pulmonol 2009 Aug 5. | | Abstract | Cystic fibrosis patients are known to produce abundant, purulent sputum consisting mainly of DNA and cellular debris. We present a case of a CF patient with recurrent airway obstruction caused by a rare condition known as plastic bronchitis (PB). PB is characterized by the formation of casts of the airways that cause obstruction. Multiple etiologies have been proposed, but to our knowledge, no CF patient has been reported in any PB classification. Histological analysis and in-vitro testing of the cast were important factors in choosing the adequate therapy in this patient. Pediatr Pulmonol. (c) 2009 Wiley-Liss, Inc. | | Language | ENG | | Pub Type(s) | JOURNAL ARTICLE
| | PubMed ID | 19658112 |
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