Q26.2 - Total anomalous pulmonary venous connection
Code
Q26.2 - Total anomalous pulmonary venous connection
[Billable] [POA Exempt]
[Billable] [POA Exempt]
Includes
- Total anomalous pulmonary venous return [TAPVR], subdiaphragmatic
- Total anomalous pulmonary venous return [TAPVR], supradiaphragmatic
Code Tree
Q00-QA1 - Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Q20-Q28 - Congenital malformations of the circulatory system
- Q26 - Congenital malformations of great veins
- Q26.0 - Congenital stenosis of vena cava
- Q26.1 - Persistent left superior vena cava
- Q26.2 - Total anomalous pulmonary venous connection
- Q26.3 - Partial anomalous pulmonary venous connection
- Q26.4 - Anomalous pulmonary venous connection, unspecified
- Q26.5 - Anomalous portal venous connection
- Q26.6 - Portal vein-hepatic artery fistula
- Q26.8 - Other congenital malformations of great veins
- Q26.9 - Congenital malformation of great vein, unspecified
- Q26 - Congenital malformations of great veins
Citation
"Q26.2 - Total Anomalous Pulmonary Venous Connection." ICD-10-CM ICD-10-CM, 10th ed., Centers for Medicare and Medicaid Services and the National Center for Health Statistics, 2027. ICD-10-CM, www.unboundmedicine.com/icd/view/ICD-10-CM/894723/all/Q26_2___Total_anomalous_pulmonary_venous_connection.
Q26.2 - Total anomalous pulmonary venous connection. ICD-10-CM ICD-10-CM. Centers for Medicare and Medicaid Services and the National Center for Health Statistics; 2027. https://www.unboundmedicine.com/icd/view/ICD-10-CM/894723/all/Q26_2___Total_anomalous_pulmonary_venous_connection. Accessed October 2, 2026.
Q26.2 - Total anomalous pulmonary venous connection. (2027). In ICD-10-CM ICD-10-CM (10th ed.). Centers for Medicare and Medicaid Services and the National Center for Health Statistics. https://www.unboundmedicine.com/icd/view/ICD-10-CM/894723/all/Q26_2___Total_anomalous_pulmonary_venous_connection
Q26.2 - Total Anomalous Pulmonary Venous Connection [Internet]. In: ICD-10-CM ICD-10-CM. Centers for Medicare and Medicaid Services and the National Center for Health Statistics; 2027. [cited 2026 October 02]. Available from: https://www.unboundmedicine.com/icd/view/ICD-10-CM/894723/all/Q26_2___Total_anomalous_pulmonary_venous_connection.
* Article titles in AMA citation format should be in sentence-case
TY - ELEC
T1 - Q26.2 - Total anomalous pulmonary venous connection
ID - 894723
BT - ICD-10-CM
UR - https://www.unboundmedicine.com/icd/view/ICD-10-CM/894723/all/Q26_2___Total_anomalous_pulmonary_venous_connection
PB - Centers for Medicare and Medicaid Services and the National Center for Health Statistics
ET - 10
DB - ICD-10-CM
DP - Unbound Medicine
ER -

ICD-10-CM

