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[Primary extramedullary plasmacytoma of the duodenum].
Swiss Surg. 1999; 5(1):6-10.SS

Abstract

INTRODUCTION

Primary extramedullary plasmacytoma (EMP) is a solitary tumor that arises outside the bone marrow in patients without clinical evidence of coexisting multiple myeloma. EMP represents only 4% of all patients with plasma cell malignancies. The tumor generally occurs in the submucosal tissue of the upper airway or oral cavity. 10% of all EMP occur in the gastrointestinal tract. Only 8 cases of EMP in the duodenum have been reported in literature.

METHOD

The authors present a case of EMP in the duodenum in a 53 year old men. The tumor was initially misdiagnosed as desmoid tumor. With a combined treatment of surgery and chemotherapy complete remission for 2 years was achieved, followed by a dissemination of the tumor in the testis, mandibular bone and ribs.

CONCLUSION

EMP is a rare differential diagnosis of an intraabdominal tumor. Diagnosis is difficult, and in most reported cases it is confirmed only postoperatively after immunohistochemical staining. Combined treatment of surgery and chemotherapy seem to offer the best potential for cure.

Authors+Show Affiliations

Medizinische Abteilung, Spital Oberengadin, Samedan. D.Gianom@ksw.chNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
English Abstract
Journal Article
Review

Language

ger

PubMed ID

10073124

Citation

Gianom, D, et al. "[Primary Extramedullary Plasmacytoma of the Duodenum]." Swiss Surgery = Schweizer Chirurgie = Chirurgie Suisse = Chirurgia Svizzera, vol. 5, no. 1, 1999, pp. 6-10.
Gianom D, Famos M, Marugg D, et al. [Primary extramedullary plasmacytoma of the duodenum]. Swiss Surg. 1999;5(1):6-10.
Gianom, D., Famos, M., Marugg, D., & Oberholzer, M. (1999). [Primary extramedullary plasmacytoma of the duodenum]. Swiss Surgery = Schweizer Chirurgie = Chirurgie Suisse = Chirurgia Svizzera, 5(1), 6-10.
Gianom D, et al. [Primary Extramedullary Plasmacytoma of the Duodenum]. Swiss Surg. 1999;5(1):6-10. PubMed PMID: 10073124.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - [Primary extramedullary plasmacytoma of the duodenum]. AU - Gianom,D, AU - Famos,M, AU - Marugg,D, AU - Oberholzer,M, PY - 1999/3/12/pubmed PY - 1999/3/12/medline PY - 1999/3/12/entrez SP - 6 EP - 10 JF - Swiss surgery = Schweizer Chirurgie = Chirurgie suisse = Chirurgia svizzera JO - Swiss Surg VL - 5 IS - 1 N2 - INTRODUCTION: Primary extramedullary plasmacytoma (EMP) is a solitary tumor that arises outside the bone marrow in patients without clinical evidence of coexisting multiple myeloma. EMP represents only 4% of all patients with plasma cell malignancies. The tumor generally occurs in the submucosal tissue of the upper airway or oral cavity. 10% of all EMP occur in the gastrointestinal tract. Only 8 cases of EMP in the duodenum have been reported in literature. METHOD: The authors present a case of EMP in the duodenum in a 53 year old men. The tumor was initially misdiagnosed as desmoid tumor. With a combined treatment of surgery and chemotherapy complete remission for 2 years was achieved, followed by a dissemination of the tumor in the testis, mandibular bone and ribs. CONCLUSION: EMP is a rare differential diagnosis of an intraabdominal tumor. Diagnosis is difficult, and in most reported cases it is confirmed only postoperatively after immunohistochemical staining. Combined treatment of surgery and chemotherapy seem to offer the best potential for cure. SN - 1023-9332 UR - https://www.unboundmedicine.com/medline/citation/10073124/[Primary_extramedullary_plasmacytoma_of_the_duodenum]_ L2 - https://medlineplus.gov/intestinalcancer.html DB - PRIME DP - Unbound Medicine ER -