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Pyloric atresia associated with epidermolysis bullosa, malrotation, and high anorectal malformation with recto-urethral fistula: a report of successful management.
Pediatr Surg Int. 1999; 15(3-4):264-5.PS

Abstract

Pyloric atresia (PA) is an uncommon anomaly that may be associated with many other congenital anomalies, the commonest of which is junctional epidermolysis bullosa (JEB). Most of the cases of PA associated with JEB (Herlitz syndrome) reported have been fatal. A case of PA associated with JEB, malrotation, and a high anorectal malformation with a rectourethral fistula, which was hitherto undescribed, was successfully managed at our institution.

Authors+Show Affiliations

Agarwala S
Department of Paediatric Surgery, All India Institute of Medical Sciences, New Delhi, India.
Goswami JK
No affiliation info available
Mitra DK
No affiliation info available

MeSH

Anus, ImperforateEpidermolysis Bullosa, JunctionalHumansInfant, NewbornIntestinesMalePylorusRectal FistulaUrethral DiseasesUrinary Fistula

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

10370040

Citation

Agarwala, S, et al. "Pyloric Atresia Associated With Epidermolysis Bullosa, Malrotation, and High Anorectal Malformation With Recto-urethral Fistula: a Report of Successful Management." Pediatric Surgery International, vol. 15, no. 3-4, 1999, pp. 264-5.
Agarwala S, Goswami JK, Mitra DK. Pyloric atresia associated with epidermolysis bullosa, malrotation, and high anorectal malformation with recto-urethral fistula: a report of successful management. Pediatr Surg Int. 1999;15(3-4):264-5.
Agarwala, S., Goswami, J. K., & Mitra, D. K. (1999). Pyloric atresia associated with epidermolysis bullosa, malrotation, and high anorectal malformation with recto-urethral fistula: a report of successful management. Pediatric Surgery International, 15(3-4), 264-5.
Agarwala S, Goswami JK, Mitra DK. Pyloric Atresia Associated With Epidermolysis Bullosa, Malrotation, and High Anorectal Malformation With Recto-urethral Fistula: a Report of Successful Management. Pediatr Surg Int. 1999;15(3-4):264-5. PubMed PMID: 10370040.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Pyloric atresia associated with epidermolysis bullosa, malrotation, and high anorectal malformation with recto-urethral fistula: a report of successful management. AU - Agarwala,S, AU - Goswami,J K, AU - Mitra,D K, PY - 1999/6/17/pubmed PY - 1999/6/17/medline PY - 1999/6/17/entrez SP - 264 EP - 5 JF - Pediatric surgery international JO - Pediatr Surg Int VL - 15 IS - 3-4 N2 - Pyloric atresia (PA) is an uncommon anomaly that may be associated with many other congenital anomalies, the commonest of which is junctional epidermolysis bullosa (JEB). Most of the cases of PA associated with JEB (Herlitz syndrome) reported have been fatal. A case of PA associated with JEB, malrotation, and a high anorectal malformation with a rectourethral fistula, which was hitherto undescribed, was successfully managed at our institution. SN - 0179-0358 UR - https://www.unboundmedicine.com/medline/citation/10370040/Pyloric_atresia_associated_with_epidermolysis_bullosa_malrotation_and_high_anorectal_malformation_with_recto_urethral_fistula:_a_report_of_successful_management_ L2 - https://doi.org/10.1007/s003830050572 DB - PRIME DP - Unbound Medicine ER -