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Congenital short-bowel; a case study and review of the literature.
Eur J Pediatr Surg. 1999 Aug; 9(4):248-50.EJ

Abstract

A congenital short bowel (CSB) is a rare entity in pediatric surgery. We present the case of a newborn boy with a total small intestinal length of 47 cm, malrotation and gastroesophageal reflux, who is 19 months old at the time of this report. Main treatment steps were Ladd's procedure, a fundoplication and long-term parenteral nutrition. We suggest that missing physiological herniation of the gut into the coelomic cavity may impair normal intestinal growth and rotation and lead to congenital short bowel. Review of all cases reported in the literature shows a considerable mortality of 88%. The limiting factor seems to be reduced motility of the short small bowel causing functional obstruction and liver failure.

Authors+Show Affiliations

Department of Pediatric Surgery, University of Graz, Medical School, Austria.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article
Review

Language

eng

PubMed ID

10532268

Citation

Schalamon, J, et al. "Congenital Short-bowel; a Case Study and Review of the Literature." European Journal of Pediatric Surgery : Official Journal of Austrian Association of Pediatric Surgery ... [et Al] = Zeitschrift Fur Kinderchirurgie, vol. 9, no. 4, 1999, pp. 248-50.
Schalamon J, Schober PH, Gallippi P, et al. Congenital short-bowel; a case study and review of the literature. Eur J Pediatr Surg. 1999;9(4):248-50.
Schalamon, J., Schober, P. H., Gallippi, P., Matthyssens, L., & Höllwarth, M. E. (1999). Congenital short-bowel; a case study and review of the literature. European Journal of Pediatric Surgery : Official Journal of Austrian Association of Pediatric Surgery ... [et Al] = Zeitschrift Fur Kinderchirurgie, 9(4), 248-50.
Schalamon J, et al. Congenital Short-bowel; a Case Study and Review of the Literature. Eur J Pediatr Surg. 1999;9(4):248-50. PubMed PMID: 10532268.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Congenital short-bowel; a case study and review of the literature. AU - Schalamon,J, AU - Schober,P H, AU - Gallippi,P, AU - Matthyssens,L, AU - Höllwarth,M E, PY - 1999/10/26/pubmed PY - 1999/10/26/medline PY - 1999/10/26/entrez SP - 248 EP - 50 JF - European journal of pediatric surgery : official journal of Austrian Association of Pediatric Surgery ... [et al] = Zeitschrift fur Kinderchirurgie JO - Eur J Pediatr Surg VL - 9 IS - 4 N2 - A congenital short bowel (CSB) is a rare entity in pediatric surgery. We present the case of a newborn boy with a total small intestinal length of 47 cm, malrotation and gastroesophageal reflux, who is 19 months old at the time of this report. Main treatment steps were Ladd's procedure, a fundoplication and long-term parenteral nutrition. We suggest that missing physiological herniation of the gut into the coelomic cavity may impair normal intestinal growth and rotation and lead to congenital short bowel. Review of all cases reported in the literature shows a considerable mortality of 88%. The limiting factor seems to be reduced motility of the short small bowel causing functional obstruction and liver failure. SN - 0939-7248 UR - https://www.unboundmedicine.com/medline/citation/10532268/Congenital_short_bowel L2 - http://www.thieme-connect.com/DOI/DOI?10.1055/s-2008-1072255 DB - PRIME DP - Unbound Medicine ER -