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Megacystis microcolon intestinal hypoperistalsis syndrome: bladder distension and pyelectasis in the fetus without anatomic outflow obstruction.
Urology. 2000 May 01; 55(5):774.U

Abstract

We report a case of a 46,XY male infant with a history of normal amniotic fluid levels who was delivered by elective cesarean section at 38.5 weeks' gestation because of progressive bladder distension, hydroureteronephrosis, and what was thought to be a dilated posterior urethra. The child died at 19 days of age of cardiovascular complications. The autopsy revealed megacystis, bilateral megaureters and pyelocaliectasis, congenital absence of ganglion cells in the bladder wall, renal dysplasia, and a microcolon. No dilation or anatomic obstruction of the posterior urethra was found. These findings strongly suggest the diagnosis of megacystis microcolon intestinal hypoperistalsis syndrome. We discuss the ultrasound findings of in utero bladder distension with hydronephrosis and one of its rare etiologies.

Authors+Show Affiliations

Division of Urology, University of California, San Diego, School of Medicine, San Diego, California, USA.No affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

10792103

Citation

Lashley, D B., et al. "Megacystis Microcolon Intestinal Hypoperistalsis Syndrome: Bladder Distension and Pyelectasis in the Fetus Without Anatomic Outflow Obstruction." Urology, vol. 55, no. 5, 2000, p. 774.
Lashley DB, Masliah E, Kaplan GW, et al. Megacystis microcolon intestinal hypoperistalsis syndrome: bladder distension and pyelectasis in the fetus without anatomic outflow obstruction. Urology. 2000;55(5):774.
Lashley, D. B., Masliah, E., Kaplan, G. W., & McAleer, I. M. (2000). Megacystis microcolon intestinal hypoperistalsis syndrome: bladder distension and pyelectasis in the fetus without anatomic outflow obstruction. Urology, 55(5), 774.
Lashley DB, et al. Megacystis Microcolon Intestinal Hypoperistalsis Syndrome: Bladder Distension and Pyelectasis in the Fetus Without Anatomic Outflow Obstruction. Urology. 2000 May 1;55(5):774. PubMed PMID: 10792103.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Megacystis microcolon intestinal hypoperistalsis syndrome: bladder distension and pyelectasis in the fetus without anatomic outflow obstruction. AU - Lashley,D B, AU - Masliah,E, AU - Kaplan,G W, AU - McAleer,I M, PY - 2000/5/3/pubmed PY - 2000/5/20/medline PY - 2000/5/3/entrez SP - 774 EP - 774 JF - Urology JO - Urology VL - 55 IS - 5 N2 - We report a case of a 46,XY male infant with a history of normal amniotic fluid levels who was delivered by elective cesarean section at 38.5 weeks' gestation because of progressive bladder distension, hydroureteronephrosis, and what was thought to be a dilated posterior urethra. The child died at 19 days of age of cardiovascular complications. The autopsy revealed megacystis, bilateral megaureters and pyelocaliectasis, congenital absence of ganglion cells in the bladder wall, renal dysplasia, and a microcolon. No dilation or anatomic obstruction of the posterior urethra was found. These findings strongly suggest the diagnosis of megacystis microcolon intestinal hypoperistalsis syndrome. We discuss the ultrasound findings of in utero bladder distension with hydronephrosis and one of its rare etiologies. SN - 1527-9995 UR - https://www.unboundmedicine.com/medline/citation/10792103/Megacystis_microcolon_intestinal_hypoperistalsis_syndrome:_bladder_distension_and_pyelectasis_in_the_fetus_without_anatomic_outflow_obstruction_ L2 - https://linkinghub.elsevier.com/retrieve/pii/S0090429500004994 DB - PRIME DP - Unbound Medicine ER -