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[Metotopic craniosynostoses].
Tidsskr Nor Laegeforen. 2000 Oct 30; 120(26):3147-50.TN

Abstract

BACKGROUND

Premature closure of the metopic suture leads to inhibited growth of the frontal bones, producing a keel-shaped forehead (trigonocephaly). Simple metopic synostosis is usually sporadic. Trigonocephalic patients account for 8-16% of the referrals to craniofacial centers, with a marked male predominance. Intracranial pressure (ICP) may be increased, whereas shunt-dependent hydrocephalus is infrequent. Infrequently, patients have intra- or extracerebral anomalies; one third have varying degrees of neuropsychological problems. The treatment is primarily surgical.

MATERIAL AND METHODS

We present two patients who during infancy developed increasingly keel-shaped foreheads, retruded orbital rims, increased biparietal diameter and close-set eyes (hypothelorism). Both had raised ICP, but normal psychomotoric development. They were operated using radical fronto-orbital surgical remodelling.

RESULTS

Recovery was uneventful. Three months post-operatively, they had pleasing cosmetic results with no symptoms of increased ICP.

INTERPRETATION

Where metopic craniosynostosis is suspected, the infant should be examined clinically with palpation of fontanelles and sutures, evaluated with respect to the shape and development of the facial skeleton, as well as by X-ray of the skull sutures. Radical fronto-orbital surgical remodelling gives a stable correction of the craniofacial deformity and generally a satisfactory cosmetic result.

Authors+Show Affiliations

Nevrokirurgisk avdeling, Rikshospitalet, Oslo. torsteinrmeling@mailcity.comNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

nor

PubMed ID

11109361

Citation

Meling, T R., et al. "[Metotopic Craniosynostoses]." Tidsskrift for Den Norske Laegeforening : Tidsskrift for Praktisk Medicin, Ny Raekke, vol. 120, no. 26, 2000, pp. 3147-50.
Meling TR, Due-Tønnessen BJ, Helseth E. [Metotopic craniosynostoses]. Tidsskr Nor Laegeforen. 2000;120(26):3147-50.
Meling, T. R., Due-Tønnessen, B. J., & Helseth, E. (2000). [Metotopic craniosynostoses]. Tidsskrift for Den Norske Laegeforening : Tidsskrift for Praktisk Medicin, Ny Raekke, 120(26), 3147-50.
Meling TR, Due-Tønnessen BJ, Helseth E. [Metotopic Craniosynostoses]. Tidsskr Nor Laegeforen. 2000 Oct 30;120(26):3147-50. PubMed PMID: 11109361.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - [Metotopic craniosynostoses]. AU - Meling,T R, AU - Due-Tønnessen,B J, AU - Helseth,E, PY - 2000/12/8/pubmed PY - 2001/2/28/medline PY - 2000/12/8/entrez SP - 3147 EP - 50 JF - Tidsskrift for den Norske laegeforening : tidsskrift for praktisk medicin, ny raekke JO - Tidsskr Nor Laegeforen VL - 120 IS - 26 N2 - BACKGROUND: Premature closure of the metopic suture leads to inhibited growth of the frontal bones, producing a keel-shaped forehead (trigonocephaly). Simple metopic synostosis is usually sporadic. Trigonocephalic patients account for 8-16% of the referrals to craniofacial centers, with a marked male predominance. Intracranial pressure (ICP) may be increased, whereas shunt-dependent hydrocephalus is infrequent. Infrequently, patients have intra- or extracerebral anomalies; one third have varying degrees of neuropsychological problems. The treatment is primarily surgical. MATERIAL AND METHODS: We present two patients who during infancy developed increasingly keel-shaped foreheads, retruded orbital rims, increased biparietal diameter and close-set eyes (hypothelorism). Both had raised ICP, but normal psychomotoric development. They were operated using radical fronto-orbital surgical remodelling. RESULTS: Recovery was uneventful. Three months post-operatively, they had pleasing cosmetic results with no symptoms of increased ICP. INTERPRETATION: Where metopic craniosynostosis is suspected, the infant should be examined clinically with palpation of fontanelles and sutures, evaluated with respect to the shape and development of the facial skeleton, as well as by X-ray of the skull sutures. Radical fronto-orbital surgical remodelling gives a stable correction of the craniofacial deformity and generally a satisfactory cosmetic result. SN - 0029-2001 UR - https://www.unboundmedicine.com/medline/citation/11109361/[Metotopic_craniosynostoses]_ DB - PRIME DP - Unbound Medicine ER -