Tags

Type your tag names separated by a space and hit enter

[Perioperative management of a neonate with aglossia-adactylia syndrome].
Masui. 2001 Jul; 50(7):773-5.M

Abstract

Aglossia-adactylia syndrome is a rare disorder characterized by aglossia and deformity of the limbs of variable degree. We managed a 2-day-old neonate with ileojejunal atresia with aglossia-adactylia syndrome. He was scheduled for the repair of the intestinal atresia, gastrostomy and palatal impression taking, under general anesthesia with sevoflurane supplemented with fentanyl. In this case we could achieve tracheal intubation by direct laryngoscopy with cricoid pressure applied, and could manage without any complications. But many of the patients with this syndrome are complicated with cleft palate and micrognathia, and we should be careful of the difficult airway at the induction of general anesthesia and aspiration during perioperative period.

Authors+Show Affiliations

Department of Anesthesiology, Osaka Medical Center and Research Institute for Maternal and Child Health, Izumi 594-1101.No affiliation info available

Pub Type(s)

Case Reports
English Abstract
Journal Article

Language

jpn

PubMed ID

11510070

Citation

Mandai, H, and K Kinouchi. "[Perioperative Management of a Neonate With Aglossia-adactylia Syndrome]." Masui. the Japanese Journal of Anesthesiology, vol. 50, no. 7, 2001, pp. 773-5.
Mandai H, Kinouchi K. [Perioperative management of a neonate with aglossia-adactylia syndrome]. Masui. 2001;50(7):773-5.
Mandai, H., & Kinouchi, K. (2001). [Perioperative management of a neonate with aglossia-adactylia syndrome]. Masui. the Japanese Journal of Anesthesiology, 50(7), 773-5.
Mandai H, Kinouchi K. [Perioperative Management of a Neonate With Aglossia-adactylia Syndrome]. Masui. 2001;50(7):773-5. PubMed PMID: 11510070.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - [Perioperative management of a neonate with aglossia-adactylia syndrome]. AU - Mandai,H, AU - Kinouchi,K, PY - 2001/8/21/pubmed PY - 2001/10/5/medline PY - 2001/8/21/entrez SP - 773 EP - 5 JF - Masui. The Japanese journal of anesthesiology JO - Masui VL - 50 IS - 7 N2 - Aglossia-adactylia syndrome is a rare disorder characterized by aglossia and deformity of the limbs of variable degree. We managed a 2-day-old neonate with ileojejunal atresia with aglossia-adactylia syndrome. He was scheduled for the repair of the intestinal atresia, gastrostomy and palatal impression taking, under general anesthesia with sevoflurane supplemented with fentanyl. In this case we could achieve tracheal intubation by direct laryngoscopy with cricoid pressure applied, and could manage without any complications. But many of the patients with this syndrome are complicated with cleft palate and micrognathia, and we should be careful of the difficult airway at the induction of general anesthesia and aspiration during perioperative period. SN - 0021-4892 UR - https://www.unboundmedicine.com/medline/citation/11510070/[Perioperative_management_of_a_neonate_with_aglossia_adactylia_syndrome]_ DB - PRIME DP - Unbound Medicine ER -