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[Anesthetic management in a patient with Simpson-Golabi-Behmel syndrome].
Masui. 2001 Oct; 50(10):1106-8.M

Abstract

We report the anesthetic management of a 4-yr-old boy with Simpson-Golabi-Behmel syndrome. This syndrome is an X-linked condition characterized by pre- and postnatal overgrowth with visceral and skeletal anomalies. Affected males have a distinctive facial appearance with wide nasal bridge, anteverted nostrils, wide-open mouth, enlarged tongue, and large protruding maxilla and jaw. Although it had been speculated preoperatively that airway management would be complicated by the macroglossia, there was no difficulty in endotracheal intubation in the present patient. Preparations for difficult airway management should be made by the anesthesiologist before induction of anesthesia.

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Authors+Show Affiliations

Tsuchiya K
Department of Anesthesiology and Critical Care Medicine, Asahikawa Medical College, Asahikawa 078-8510.
Takahata O
No affiliation info available
Sengoku K
No affiliation info available
Hamada I
No affiliation info available
Suzuki A
No affiliation info available
Iwasaki H
No affiliation info available

MeSH

Abnormalities, MultipleAnesthesia, InhalationChild, PreschoolFaceGenetic LinkageGigantismHumansIntraoperative CareMacroglossiaMaleSyndromeTongueX Chromosome

Pub Type(s)

Case Reports
English Abstract
Journal Article

Language

jpn

PubMed ID

11712343

Citation

Tsuchiya, K, et al. "[Anesthetic Management in a Patient With Simpson-Golabi-Behmel Syndrome]." Masui. the Japanese Journal of Anesthesiology, vol. 50, no. 10, 2001, pp. 1106-8.
Tsuchiya K, Takahata O, Sengoku K, et al. [Anesthetic management in a patient with Simpson-Golabi-Behmel syndrome]. Masui. 2001;50(10):1106-8.
Tsuchiya, K., Takahata, O., Sengoku, K., Hamada, I., Suzuki, A., & Iwasaki, H. (2001). [Anesthetic management in a patient with Simpson-Golabi-Behmel syndrome]. Masui. the Japanese Journal of Anesthesiology, 50(10), 1106-8.
Tsuchiya K, et al. [Anesthetic Management in a Patient With Simpson-Golabi-Behmel Syndrome]. Masui. 2001;50(10):1106-8. PubMed PMID: 11712343.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - [Anesthetic management in a patient with Simpson-Golabi-Behmel syndrome]. AU - Tsuchiya,K, AU - Takahata,O, AU - Sengoku,K, AU - Hamada,I, AU - Suzuki,A, AU - Iwasaki,H, PY - 2001/11/20/pubmed PY - 2002/1/5/medline PY - 2001/11/20/entrez SP - 1106 EP - 8 JF - Masui. The Japanese journal of anesthesiology JO - Masui VL - 50 IS - 10 N2 - We report the anesthetic management of a 4-yr-old boy with Simpson-Golabi-Behmel syndrome. This syndrome is an X-linked condition characterized by pre- and postnatal overgrowth with visceral and skeletal anomalies. Affected males have a distinctive facial appearance with wide nasal bridge, anteverted nostrils, wide-open mouth, enlarged tongue, and large protruding maxilla and jaw. Although it had been speculated preoperatively that airway management would be complicated by the macroglossia, there was no difficulty in endotracheal intubation in the present patient. Preparations for difficult airway management should be made by the anesthesiologist before induction of anesthesia. SN - 0021-4892 UR - https://www.unboundmedicine.com/medline/citation/11712343/[Anesthetic_management_in_a_patient_with_Simpson_Golabi_Behmel_syndrome]_ L2 - https://www.medicalonline.jp/meteo_linkout.php?issn=0021-4892&volume=50&issue=10&spage=1106 DB - PRIME DP - Unbound Medicine ER -