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Familial visceral myopathy with carcinoma of unknown primary.
Ann Clin Lab Sci. 2002 Winter; 32(1):93-7.AC

Abstract

We report an autopsy case of a 35-yr-old man with familial visceral myopathy, a cause of primary intestinal pseudo-obstruction. The patient died from complications of familial visceral myopathy, sepsis, and generalized signet-ring cell carcinomatosis. The patient had massive distension of the large and small intestines, a dilated thickened esophagus, and fibroneoplastic adhesions between intra-abdominal and thoracic structures. This case provides an observation, not previously described in cases of familial visceral myopathy, which is fibrosis and atrophy of the outer longitudinal smooth muscle of the small bowel, alternating to involve only the inner smooth muscle layer of the large bowel. This case shows how a malignant neoplasm can compound the pathology of familial visceral myopathy.

Authors+Show Affiliations

Department of Pathology, North Shore University Hospital, Manhasset, New York 11030, USA. farbodarv@cs.comNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

11848624

Citation

Darvishian, Farbod, and Kevin Basham. "Familial Visceral Myopathy With Carcinoma of Unknown Primary." Annals of Clinical and Laboratory Science, vol. 32, no. 1, 2002, pp. 93-7.
Darvishian F, Basham K. Familial visceral myopathy with carcinoma of unknown primary. Ann Clin Lab Sci. 2002;32(1):93-7.
Darvishian, F., & Basham, K. (2002). Familial visceral myopathy with carcinoma of unknown primary. Annals of Clinical and Laboratory Science, 32(1), 93-7.
Darvishian F, Basham K. Familial Visceral Myopathy With Carcinoma of Unknown Primary. Ann Clin Lab Sci. 2002;32(1):93-7. PubMed PMID: 11848624.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Familial visceral myopathy with carcinoma of unknown primary. AU - Darvishian,Farbod, AU - Basham,Kevin, PY - 2002/2/19/pubmed PY - 2002/8/7/medline PY - 2002/2/19/entrez SP - 93 EP - 7 JF - Annals of clinical and laboratory science JO - Ann Clin Lab Sci VL - 32 IS - 1 N2 - We report an autopsy case of a 35-yr-old man with familial visceral myopathy, a cause of primary intestinal pseudo-obstruction. The patient died from complications of familial visceral myopathy, sepsis, and generalized signet-ring cell carcinomatosis. The patient had massive distension of the large and small intestines, a dilated thickened esophagus, and fibroneoplastic adhesions between intra-abdominal and thoracic structures. This case provides an observation, not previously described in cases of familial visceral myopathy, which is fibrosis and atrophy of the outer longitudinal smooth muscle of the small bowel, alternating to involve only the inner smooth muscle layer of the large bowel. This case shows how a malignant neoplasm can compound the pathology of familial visceral myopathy. SN - 0091-7370 UR - https://www.unboundmedicine.com/medline/citation/11848624/Familial_visceral_myopathy_with_carcinoma_of_unknown_primary_ L2 - http://www.annclinlabsci.org/cgi/pmidlookup?view=long&pmid=11848624 DB - PRIME DP - Unbound Medicine ER -