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Primary intraspinal primitive neuroectodermal tumor (PNET): a rare occurrence.
Neurol India. 2002 Mar; 50(1):75-80.NI

Abstract

The concept of primitive neuroectodermal tumors (PNETs) has been evolving for many years, as has been its nomenclature. A 5 year old boy presented with pain in lower cervicodorsal region and left leg. Preoperative MRI of the spine and paravertebral region revealed a hyperintense lobulated lesion extending from D1-D4 with a large intraspinal and thoracic component. A total removal of tumor was achieved via a dorsal laminectomy and right posterolateral thoracotomy. The pathological findings were consistent with PNET. Post operative neurological examination had been unremarkable. Six months follow up scan showed no recurrence. A review of the literature shows that only 18 cases of primary intraspinal PNETs have been reported to date and the present case is exclusive, in which the tumor was thoracic, extradural in location and the child is alive at 8 months of follow up, with no evidence of tumor recurrence/metastasis. Primary intraspinal PNETs are rare tumors and carry a poor prognosis. Newer modalities of treatment should be tried to improve survival.

Authors+Show Affiliations

Department of Neurosurgery, Jaslok Hospital and Research Centre, Mumbai, 400026, India. drsurbhi@netscape.netNo affiliation info available

Pub Type(s)

Case Reports
Journal Article
Review

Language

eng

PubMed ID

11960157

Citation

Virani, M J., and S Jain. "Primary Intraspinal Primitive Neuroectodermal Tumor (PNET): a Rare Occurrence." Neurology India, vol. 50, no. 1, 2002, pp. 75-80.
Virani MJ, Jain S. Primary intraspinal primitive neuroectodermal tumor (PNET): a rare occurrence. Neurol India. 2002;50(1):75-80.
Virani, M. J., & Jain, S. (2002). Primary intraspinal primitive neuroectodermal tumor (PNET): a rare occurrence. Neurology India, 50(1), 75-80.
Virani MJ, Jain S. Primary Intraspinal Primitive Neuroectodermal Tumor (PNET): a Rare Occurrence. Neurol India. 2002;50(1):75-80. PubMed PMID: 11960157.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Primary intraspinal primitive neuroectodermal tumor (PNET): a rare occurrence. AU - Virani,M J, AU - Jain,S, PY - 2002/4/18/pubmed PY - 2002/5/8/medline PY - 2002/4/18/entrez SP - 75 EP - 80 JF - Neurology India JO - Neurol India VL - 50 IS - 1 N2 - The concept of primitive neuroectodermal tumors (PNETs) has been evolving for many years, as has been its nomenclature. A 5 year old boy presented with pain in lower cervicodorsal region and left leg. Preoperative MRI of the spine and paravertebral region revealed a hyperintense lobulated lesion extending from D1-D4 with a large intraspinal and thoracic component. A total removal of tumor was achieved via a dorsal laminectomy and right posterolateral thoracotomy. The pathological findings were consistent with PNET. Post operative neurological examination had been unremarkable. Six months follow up scan showed no recurrence. A review of the literature shows that only 18 cases of primary intraspinal PNETs have been reported to date and the present case is exclusive, in which the tumor was thoracic, extradural in location and the child is alive at 8 months of follow up, with no evidence of tumor recurrence/metastasis. Primary intraspinal PNETs are rare tumors and carry a poor prognosis. Newer modalities of treatment should be tried to improve survival. SN - 0028-3886 UR - https://www.unboundmedicine.com/medline/citation/11960157/Primary_intraspinal_primitive_neuroectodermal_tumor__PNET_:_a_rare_occurrence_ L2 - http://www.neurologyindia.com/article.asp?issn=0028-3886;year=2002;volume=50;issue=1;spage=75;epage=80;aulast=Virani DB - PRIME DP - Unbound Medicine ER -