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Novel dental anomalies associated with congenital contractural arachnodactyly: a case report.
Pediatr Dent. 2003 Sep-Oct; 25(5):501-4.PD

Abstract

Congenital contractural arachnodactyly (CCA) is an inherited disorder of connective tissue similar to Marfan's syndrome. The craniofacial and oral features of a young girl with CCA are described. The patient has the typical features of CCA as well as some additional dental anomalies which have not previously been reported with this syndrome. These include banded pitted enamel hypoplasia and hypomineralization, long, spindly tapered roots, and pulp canal obliteration with multiple pulp stones. Dentists must be aware of the clinical features of a patient's syndrome to determine whether there are implications for dental treatment such as a need for antibiotic prophylaxis. It is important to exclude Marfan's syndrome as a differential diagnosis for CCA because the former has more associated complications and a less favorable prognosis.

Authors+Show Affiliations

Department of Oral Sciences, Faculty of Dentistry, University of Otago, Dunedin, New Zealand. katie.ayers@stonebow.otago.ac.nzNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

14649616

Citation

Ayers, Kathryn Marina Sherwood, and Bernadette Kathleen Drummond. "Novel Dental Anomalies Associated With Congenital Contractural Arachnodactyly: a Case Report." Pediatric Dentistry, vol. 25, no. 5, 2003, pp. 501-4.
Ayers KM, Drummond BK. Novel dental anomalies associated with congenital contractural arachnodactyly: a case report. Pediatr Dent. 2003;25(5):501-4.
Ayers, K. M., & Drummond, B. K. (2003). Novel dental anomalies associated with congenital contractural arachnodactyly: a case report. Pediatric Dentistry, 25(5), 501-4.
Ayers KM, Drummond BK. Novel Dental Anomalies Associated With Congenital Contractural Arachnodactyly: a Case Report. Pediatr Dent. 2003 Sep-Oct;25(5):501-4. PubMed PMID: 14649616.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Novel dental anomalies associated with congenital contractural arachnodactyly: a case report. AU - Ayers,Kathryn Marina Sherwood, AU - Drummond,Bernadette Kathleen, PY - 2003/12/3/pubmed PY - 2004/1/17/medline PY - 2003/12/3/entrez SP - 501 EP - 4 JF - Pediatric dentistry JO - Pediatr Dent VL - 25 IS - 5 N2 - Congenital contractural arachnodactyly (CCA) is an inherited disorder of connective tissue similar to Marfan's syndrome. The craniofacial and oral features of a young girl with CCA are described. The patient has the typical features of CCA as well as some additional dental anomalies which have not previously been reported with this syndrome. These include banded pitted enamel hypoplasia and hypomineralization, long, spindly tapered roots, and pulp canal obliteration with multiple pulp stones. Dentists must be aware of the clinical features of a patient's syndrome to determine whether there are implications for dental treatment such as a need for antibiotic prophylaxis. It is important to exclude Marfan's syndrome as a differential diagnosis for CCA because the former has more associated complications and a less favorable prognosis. SN - 0164-1263 UR - https://www.unboundmedicine.com/medline/citation/14649616/Novel_dental_anomalies_associated_with_congenital_contractural_arachnodactyly:_a_case_report_ L2 - http://www.diseaseinfosearch.org/result/1796 DB - PRIME DP - Unbound Medicine ER -