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Rendu-Osler-Weber disease with a giant intracerebral varix secondary to a high-flow pial AVF: case report.
Surg Neurol. 2004 Apr; 61(4):353-6.SN

Abstract

BACKGROUND

Intracranial varices are rare and most are associated with vein of Galen arteriovenous malformations (AVM) or fistulas (AVF).

DESCRIPTION

A 43-year-old left-handed man presented with right hemihypesthesia and spastic gait. Neuroradiological examination revealed a spinal AVF and a giant intracerebral varix associated with a high-flow pial AVF. He had recurrent episodes of nasal bleeding, which were also confirmed in his mother's medical history, and telangiectases in the tip of his tongue and fingers. He was diagnosed with Rendu-Osler-Weber disease. After resection of the spinal AVF that produced his symptoms, we surgically exposed and obliterated the giant varix and AVF under intra- and postoperative hypotension and mild barbiturate therapy. The arteriovenous shunt was completely obliterated without hyperperfusion of the surrounding brain.

CONCLUSION

This is an extremely rare case of Rendu-Osler-Weber disease with a giant intracerebral varix secondary to a high-flow pial AVF that did not involve the vein of Galen.

Authors+Show Affiliations

Oda M
Department of Neurosurgery, Kyoto University Graduate School of Medicine, Kyoto, Japan.
Takahashi JA
No affiliation info available
Hashimoto N
No affiliation info available
Koyama T
No affiliation info available

MeSH

AdultArteriovenous FistulaBrainEpistaxisGait Disorders, NeurologicHumansIntracranial Arteriovenous MalformationsMaleRecurrenceTelangiectasisVaricose Veins

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

15031072

Citation

Oda, Masashi, et al. "Rendu-Osler-Weber Disease With a Giant Intracerebral Varix Secondary to a High-flow Pial AVF: Case Report." Surgical Neurology, vol. 61, no. 4, 2004, pp. 353-6.
Oda M, Takahashi JA, Hashimoto N, et al. Rendu-Osler-Weber disease with a giant intracerebral varix secondary to a high-flow pial AVF: case report. Surg Neurol. 2004;61(4):353-6.
Oda, M., Takahashi, J. A., Hashimoto, N., & Koyama, T. (2004). Rendu-Osler-Weber disease with a giant intracerebral varix secondary to a high-flow pial AVF: case report. Surgical Neurology, 61(4), 353-6.
Oda M, et al. Rendu-Osler-Weber Disease With a Giant Intracerebral Varix Secondary to a High-flow Pial AVF: Case Report. Surg Neurol. 2004;61(4):353-6. PubMed PMID: 15031072.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Rendu-Osler-Weber disease with a giant intracerebral varix secondary to a high-flow pial AVF: case report. AU - Oda,Masashi, AU - Takahashi,Jun A, AU - Hashimoto,Nobuo, AU - Koyama,Tsunemaro, PY - 2002/12/23/received PY - 2003/05/22/accepted PY - 2004/3/20/pubmed PY - 2004/4/3/medline PY - 2004/3/20/entrez SP - 353 EP - 6 JF - Surgical neurology JO - Surg Neurol VL - 61 IS - 4 N2 - BACKGROUND: Intracranial varices are rare and most are associated with vein of Galen arteriovenous malformations (AVM) or fistulas (AVF). DESCRIPTION: A 43-year-old left-handed man presented with right hemihypesthesia and spastic gait. Neuroradiological examination revealed a spinal AVF and a giant intracerebral varix associated with a high-flow pial AVF. He had recurrent episodes of nasal bleeding, which were also confirmed in his mother's medical history, and telangiectases in the tip of his tongue and fingers. He was diagnosed with Rendu-Osler-Weber disease. After resection of the spinal AVF that produced his symptoms, we surgically exposed and obliterated the giant varix and AVF under intra- and postoperative hypotension and mild barbiturate therapy. The arteriovenous shunt was completely obliterated without hyperperfusion of the surrounding brain. CONCLUSION: This is an extremely rare case of Rendu-Osler-Weber disease with a giant intracerebral varix secondary to a high-flow pial AVF that did not involve the vein of Galen. SN - 0090-3019 UR - https://www.unboundmedicine.com/medline/citation/15031072/Rendu_Osler_Weber_disease_with_a_giant_intracerebral_varix_secondary_to_a_high_flow_pial_AVF:_case_report_ DB - PRIME DP - Unbound Medicine ER -