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Behçet's disease: external ear involvement.
Int J Pediatr Otorhinolaryngol. 2004 Jun; 68(6):817-21.IJ

Abstract

Behçet's disease is an autoimmune vasculitis characterized by recurrent episodes of oral and genital ulcerations, skin lesions and uveitis. It also affects neurological, vascular, articular and gastrointestinal systems. Although etiology and pathogenesis are under investigation, studies have shown that HLA-B51 influences genetic susceptibility. The development of the disease is associated to neutrophil activation. Treatment depends on the severity of the disease and immunosuppressive drugs are often used. Blindness and dementia are long-term concerns. We report an unprecedented case of a child with Behçet's disease presenting a skin lesion with necrosis of the external ear canal, facial paresis, Horner's syndrome and rupture of the internal carotid artery.

Authors+Show Affiliations

Miura MS
Department of Ophthalmology and Otorhinolaryngology at Fundação Faculdade Federal de Ciências Médicas de Porto Alegre, Division of Pediatric Otorhinolaryngology at Santo Antônio Children's Hospital, Porto Alegre, RS, Brazil.
Lubianca Neto JF
No affiliation info available
Krumenauer RC
No affiliation info available
Prates K
No affiliation info available
de Castro R
No affiliation info available
Saffer M
No affiliation info available

MeSH

Behcet SyndromeCarotid Artery DiseasesCarotid Artery, InternalChild, PreschoolDiagnosis, DifferentialEar DiseasesEar, ExternalFacial ParalysisFemaleHumansNecrosisRupture, Spontaneous

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

15126024

Citation

Miura, Maurício Schreiner, et al. "Behçet's Disease: External Ear Involvement." International Journal of Pediatric Otorhinolaryngology, vol. 68, no. 6, 2004, pp. 817-21.
Miura MS, Lubianca Neto JF, Krumenauer RC, et al. Behçet's disease: external ear involvement. Int J Pediatr Otorhinolaryngol. 2004;68(6):817-21.
Miura, M. S., Lubianca Neto, J. F., Krumenauer, R. C., Prates, K., de Castro, R., & Saffer, M. (2004). Behçet's disease: external ear involvement. International Journal of Pediatric Otorhinolaryngology, 68(6), 817-21.
Miura MS, et al. Behçet's Disease: External Ear Involvement. Int J Pediatr Otorhinolaryngol. 2004;68(6):817-21. PubMed PMID: 15126024.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Behçet's disease: external ear involvement. AU - Miura,Maurício Schreiner, AU - Lubianca Neto,José Faibes, AU - Krumenauer,Rita Carolina, AU - Prates,Kátia, AU - de Castro,Rodrigo, AU - Saffer,Moacyr, PY - 2003/08/05/received PY - 2003/12/22/revised PY - 2003/12/22/accepted PY - 2004/5/6/pubmed PY - 2004/10/13/medline PY - 2004/5/6/entrez SP - 817 EP - 21 JF - International journal of pediatric otorhinolaryngology JO - Int J Pediatr Otorhinolaryngol VL - 68 IS - 6 N2 - Behçet's disease is an autoimmune vasculitis characterized by recurrent episodes of oral and genital ulcerations, skin lesions and uveitis. It also affects neurological, vascular, articular and gastrointestinal systems. Although etiology and pathogenesis are under investigation, studies have shown that HLA-B51 influences genetic susceptibility. The development of the disease is associated to neutrophil activation. Treatment depends on the severity of the disease and immunosuppressive drugs are often used. Blindness and dementia are long-term concerns. We report an unprecedented case of a child with Behçet's disease presenting a skin lesion with necrosis of the external ear canal, facial paresis, Horner's syndrome and rupture of the internal carotid artery. SN - 0165-5876 UR - https://www.unboundmedicine.com/medline/citation/15126024/Behçet's_disease:_external_ear_involvement_ DB - PRIME DP - Unbound Medicine ER -