Malignant angioendotheliomatosis mimicking systemic necrotizing vasculitis.J Rheumatol. 1992 Jul; 19(7):1133-5.JR
Abstract
Malignant angioendotheliomatosis is a rare disease characterized by an intravascular proliferation of atypical mononuclear cells. Manifestations result from occlusion of small blood vessels. Multiple organ systems are involved and the clinical presentation resembles a systemic necrotizing vasculitis with skin and central nervous system most commonly involved. The clinical course is characterized by progressive organ failure with death usually within 2 years after presentation. Based on its assumed origin as an intravascular lymphoma, patients may respond to chemotherapy.
Pub Type(s)
Case Reports
Journal Article
Language
eng
PubMed ID
1512773
Citation
Kao, N L., et al. "Malignant Angioendotheliomatosis Mimicking Systemic Necrotizing Vasculitis." The Journal of Rheumatology, vol. 19, no. 7, 1992, pp. 1133-5.
Kao NL, Broy S, Tillawi I. Malignant angioendotheliomatosis mimicking systemic necrotizing vasculitis. J Rheumatol. 1992;19(7):1133-5.
Kao, N. L., Broy, S., & Tillawi, I. (1992). Malignant angioendotheliomatosis mimicking systemic necrotizing vasculitis. The Journal of Rheumatology, 19(7), 1133-5.
Kao NL, Broy S, Tillawi I. Malignant Angioendotheliomatosis Mimicking Systemic Necrotizing Vasculitis. J Rheumatol. 1992;19(7):1133-5. PubMed PMID: 1512773.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR
T1 - Malignant angioendotheliomatosis mimicking systemic necrotizing vasculitis.
AU - Kao,N L,
AU - Broy,S,
AU - Tillawi,I,
PY - 1992/7/1/pubmed
PY - 1992/7/1/medline
PY - 1992/7/1/entrez
SP - 1133
EP - 5
JF - The Journal of rheumatology
JO - J Rheumatol
VL - 19
IS - 7
N2 - Malignant angioendotheliomatosis is a rare disease characterized by an intravascular proliferation of atypical mononuclear cells. Manifestations result from occlusion of small blood vessels. Multiple organ systems are involved and the clinical presentation resembles a systemic necrotizing vasculitis with skin and central nervous system most commonly involved. The clinical course is characterized by progressive organ failure with death usually within 2 years after presentation. Based on its assumed origin as an intravascular lymphoma, patients may respond to chemotherapy.
SN - 0315-162X
UR - https://www.unboundmedicine.com/medline/citation/1512773/Malignant_angioendotheliomatosis_mimicking_systemic_necrotizing_vasculitis_
L2 - http://www.diseaseinfosearch.org/result/9633
DB - PRIME
DP - Unbound Medicine
ER -