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Comparison of the craniofacial characteristics of two syndromes associated with the Pierre Robin sequence.
Cleft Palate Craniofac J. 1992 May; 29(3):210-9.CP

Abstract

The craniofacial characteristics of two syndromes commonly associated with Robin sequence were compared for 49 subjects. Lateral cephalograms were analyzed for four groupings: Group I--Stickler syndrome with versus without Robin, Group II--velocardiofacial (VCF) syndrome with versus without Robin, Group III--Stickler without Robin compared to VCF without Robin, and Group IV--Stickler with Robin compared to VCF with Robin. Thirty-two skeletal and 18 soft tissue measurements were compared. In Group I, three skeletal measurements were significantly different (SNA, SNB, and SNPg). In Group II, no significant difference was found for any of the 50 measurements. In Group III, a significant difference was demonstrated for seven parameters (one skeletal, six pharyngeal and airway). In Group IV, two skeletal and eight airway measures were significantly different. The findings indicate that the relative maxillary and mandibular retrognathia observed in Stickler/Robin patients may predispose them to the Robin sequence and vice versa; the Robin features in VCF may be caused by hypotonia rather than any craniofacial or physical obstruction of the airway; Stickler and VCF are similar in craniofacial morphology but show marked differences in pharyngeal and airway morphology; and cephalometrics should not be the sole prognosticator of the Robin sequence and its association with Stickler and VCF.

Authors+Show Affiliations

Albert Einstein College of Medicine, Bronx, New York.No affiliation info available

Pub Type(s)

Comparative Study
Journal Article

Language

eng

PubMed ID

1591253

Citation

Glander, K, and G J. Cisneros. "Comparison of the Craniofacial Characteristics of Two Syndromes Associated With the Pierre Robin Sequence." The Cleft Palate-craniofacial Journal : Official Publication of the American Cleft Palate-Craniofacial Association, vol. 29, no. 3, 1992, pp. 210-9.
Glander K, Cisneros GJ. Comparison of the craniofacial characteristics of two syndromes associated with the Pierre Robin sequence. Cleft Palate Craniofac J. 1992;29(3):210-9.
Glander, K., & Cisneros, G. J. (1992). Comparison of the craniofacial characteristics of two syndromes associated with the Pierre Robin sequence. The Cleft Palate-craniofacial Journal : Official Publication of the American Cleft Palate-Craniofacial Association, 29(3), 210-9.
Glander K, Cisneros GJ. Comparison of the Craniofacial Characteristics of Two Syndromes Associated With the Pierre Robin Sequence. Cleft Palate Craniofac J. 1992;29(3):210-9. PubMed PMID: 1591253.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Comparison of the craniofacial characteristics of two syndromes associated with the Pierre Robin sequence. AU - Glander,K,2nd AU - Cisneros,G J, PY - 1992/5/1/pubmed PY - 1992/5/1/medline PY - 1992/5/1/entrez SP - 210 EP - 9 JF - The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association JO - Cleft Palate Craniofac J VL - 29 IS - 3 N2 - The craniofacial characteristics of two syndromes commonly associated with Robin sequence were compared for 49 subjects. Lateral cephalograms were analyzed for four groupings: Group I--Stickler syndrome with versus without Robin, Group II--velocardiofacial (VCF) syndrome with versus without Robin, Group III--Stickler without Robin compared to VCF without Robin, and Group IV--Stickler with Robin compared to VCF with Robin. Thirty-two skeletal and 18 soft tissue measurements were compared. In Group I, three skeletal measurements were significantly different (SNA, SNB, and SNPg). In Group II, no significant difference was found for any of the 50 measurements. In Group III, a significant difference was demonstrated for seven parameters (one skeletal, six pharyngeal and airway). In Group IV, two skeletal and eight airway measures were significantly different. The findings indicate that the relative maxillary and mandibular retrognathia observed in Stickler/Robin patients may predispose them to the Robin sequence and vice versa; the Robin features in VCF may be caused by hypotonia rather than any craniofacial or physical obstruction of the airway; Stickler and VCF are similar in craniofacial morphology but show marked differences in pharyngeal and airway morphology; and cephalometrics should not be the sole prognosticator of the Robin sequence and its association with Stickler and VCF. SN - 1055-6656 UR - https://www.unboundmedicine.com/medline/citation/1591253/Comparison_of_the_craniofacial_characteristics_of_two_syndromes_associated_with_the_Pierre_Robin_sequence_ L2 - https://journals.sagepub.com/doi/10.1597/1545-1569_1992_029_0210_cotcco_2.3.co_2?url_ver=Z39.88-2003&rfr_id=ori:rid:crossref.org&rfr_dat=cr_pub=pubmed DB - PRIME DP - Unbound Medicine ER -