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Rendu-Osler-Weber syndrome presenting with pulmonary arteriovenous fistula.
Australas Radiol. 2005 Jun; 49(3):242-5.AR

Abstract

A pulmonary arteriovenous fistula is an abnormal connection between pulmonary arteries and veins. Patients with Rendu-Osler-Weber syndrome may present with this vascular malformation, which is a typical finding of the disease. Approximately 5-15% of Rendu-Osler-Weber syndrome patients have pulmonary arteriovenous malformations (AVM) and there is usually a family history of AVM in these patients. The malformations are usually located in the lower lobes. In this paper, I describe a 49-year-old male patient with dyspnoea, cough, haemoptysis and epistaxis. Physical examination showed nasal telangiectasias, cyanosis of the lips and nails, and a systolic bruit over the left lung. Chest X-ray revealed a 5-cm mass in the left lower lobe and after magnetic resonance examination, together with 3-D magnetic resonance angiography, it was demonstrated to be a pulmonary arteriovenous fistula. The history of a niece with a similiar history of suspected pulmonary arteriovenous fistula led me to consider the possibility of Rendu-Osler-Weber syndrome presenting with a pulmonary arteriovenous fistula.

Authors+Show Affiliations

Halefoglu AM
Department of Radiology, Sisli Etfal Training and Research Hospital, Istanbul, Turkey. halefoglu@hotmail.com

MeSH

Arteriovenous FistulaArteriovenous MalformationsContrast MediaGadolinium DTPAHumansLungMagnetic Resonance AngiographyMagnetic Resonance ImagingMaleMiddle AgedPulmonary ArteryPulmonary VeinsTelangiectasia, Hereditary Hemorrhagic

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

15932469

Citation

Halefoglu, A M.. "Rendu-Osler-Weber Syndrome Presenting With Pulmonary Arteriovenous Fistula." Australasian Radiology, vol. 49, no. 3, 2005, pp. 242-5.
Halefoglu AM. Rendu-Osler-Weber syndrome presenting with pulmonary arteriovenous fistula. Australas Radiol. 2005;49(3):242-5.
Halefoglu, A. M. (2005). Rendu-Osler-Weber syndrome presenting with pulmonary arteriovenous fistula. Australasian Radiology, 49(3), 242-5.
Halefoglu AM. Rendu-Osler-Weber Syndrome Presenting With Pulmonary Arteriovenous Fistula. Australas Radiol. 2005;49(3):242-5. PubMed PMID: 15932469.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Rendu-Osler-Weber syndrome presenting with pulmonary arteriovenous fistula. A1 - Halefoglu,A M, PY - 2005/6/4/pubmed PY - 2005/7/27/medline PY - 2005/6/4/entrez SP - 242 EP - 5 JF - Australasian radiology JO - Australas Radiol VL - 49 IS - 3 N2 - A pulmonary arteriovenous fistula is an abnormal connection between pulmonary arteries and veins. Patients with Rendu-Osler-Weber syndrome may present with this vascular malformation, which is a typical finding of the disease. Approximately 5-15% of Rendu-Osler-Weber syndrome patients have pulmonary arteriovenous malformations (AVM) and there is usually a family history of AVM in these patients. The malformations are usually located in the lower lobes. In this paper, I describe a 49-year-old male patient with dyspnoea, cough, haemoptysis and epistaxis. Physical examination showed nasal telangiectasias, cyanosis of the lips and nails, and a systolic bruit over the left lung. Chest X-ray revealed a 5-cm mass in the left lower lobe and after magnetic resonance examination, together with 3-D magnetic resonance angiography, it was demonstrated to be a pulmonary arteriovenous fistula. The history of a niece with a similiar history of suspected pulmonary arteriovenous fistula led me to consider the possibility of Rendu-Osler-Weber syndrome presenting with a pulmonary arteriovenous fistula. SN - 0004-8461 UR - https://www.unboundmedicine.com/medline/citation/15932469/Rendu_Osler_Weber_syndrome_presenting_with_pulmonary_arteriovenous_fistula_ DB - PRIME DP - Unbound Medicine ER -