Tags

Type your tag names separated by a space and hit enter

[Bronchospasm during anesthesia in a patient with Pena-Shokeir syndrome].
Masui. 2005 Oct; 54(10):1146-8.M

Abstract

A 3-month-old boy with Pena-Shokeir syndrome underwent tracheotomy under general anesthesia. Patients with this syndrome may present anesthetic problems involving difficulties in tracheal intubation, possibilities of malignant hyperthermia, as well as perioperative respiratory complications related to hypoplasia of the lung. General anesthesia was induced and maintained with sevoflurane (2-3%) and nitrous oxide (0-50%) in oxygen (50-100%). The patient developed bronchospasm during tracheotomy. Atropine and epinephrine were administered intravenously and 5% sevoflurane was inhaled. The bronchospasm was improved gradually and surgery was successfully finished. Pena-Shokeir syndrome is an uncommon disease first reported by Pena & Shokeir in 1974 and characterized by congenital multiple arthrogryposis, characteristic facies, camptodactyly and pulmonary hypoplasia. In the perioperative management for a patient with Pena-Shokeir syndrome, special attention should be paid to abnormalities in the upper and lower respiratory systems, especially bronchospasm.

Authors+Show Affiliations

Department of Anesthesiology, Tokushima University School of Medicine, Tokushima.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
English Abstract
Journal Article

Language

jpn

PubMed ID

16231771

Citation

Nakamura, Akiyo, et al. "[Bronchospasm During Anesthesia in a Patient With Pena-Shokeir Syndrome]." Masui. the Japanese Journal of Anesthesiology, vol. 54, no. 10, 2005, pp. 1146-8.
Nakamura A, Kawahito S, Katayama T, et al. [Bronchospasm during anesthesia in a patient with Pena-Shokeir syndrome]. Masui. 2005;54(10):1146-8.
Nakamura, A., Kawahito, S., Katayama, T., Kawano, T., Nitta, K., Inui, D., Kitahata, H., & Oshita, S. (2005). [Bronchospasm during anesthesia in a patient with Pena-Shokeir syndrome]. Masui. the Japanese Journal of Anesthesiology, 54(10), 1146-8.
Nakamura A, et al. [Bronchospasm During Anesthesia in a Patient With Pena-Shokeir Syndrome]. Masui. 2005;54(10):1146-8. PubMed PMID: 16231771.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - [Bronchospasm during anesthesia in a patient with Pena-Shokeir syndrome]. AU - Nakamura,Akiyo, AU - Kawahito,Shinji, AU - Katayama,Toshiko, AU - Kawano,Takashi, AU - Nitta,Kazuhito, AU - Inui,Daisuke, AU - Kitahata,Hiroshi, AU - Oshita,Shuzo, PY - 2005/10/20/pubmed PY - 2005/11/8/medline PY - 2005/10/20/entrez SP - 1146 EP - 8 JF - Masui. The Japanese journal of anesthesiology JO - Masui VL - 54 IS - 10 N2 - A 3-month-old boy with Pena-Shokeir syndrome underwent tracheotomy under general anesthesia. Patients with this syndrome may present anesthetic problems involving difficulties in tracheal intubation, possibilities of malignant hyperthermia, as well as perioperative respiratory complications related to hypoplasia of the lung. General anesthesia was induced and maintained with sevoflurane (2-3%) and nitrous oxide (0-50%) in oxygen (50-100%). The patient developed bronchospasm during tracheotomy. Atropine and epinephrine were administered intravenously and 5% sevoflurane was inhaled. The bronchospasm was improved gradually and surgery was successfully finished. Pena-Shokeir syndrome is an uncommon disease first reported by Pena & Shokeir in 1974 and characterized by congenital multiple arthrogryposis, characteristic facies, camptodactyly and pulmonary hypoplasia. In the perioperative management for a patient with Pena-Shokeir syndrome, special attention should be paid to abnormalities in the upper and lower respiratory systems, especially bronchospasm. SN - 0021-4892 UR - https://www.unboundmedicine.com/medline/citation/16231771/[Bronchospasm_during_anesthesia_in_a_patient_with_Pena_Shokeir_syndrome]_ DB - PRIME DP - Unbound Medicine ER -