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Cardiovascular abnormalities and arrhythmias in patients with Ondine's curse (congenital central hypoventilation) syndrome.
Pacing Clin Electrophysiol. 2005 Nov; 28(11):1226-30.PC

Abstract

Patients with congenital central hypoventilation syndrome (CCHS) (Ondine's curse syndrome) have impaired autonomic control of ventilation with intact voluntary control of respiration. Autonomic dysfunction and cardiac abnormalities are common in CCHS. Bradyarrhythmias are life-threatening and often require pacemaker insertion. We presented a case of a patient with CCHS suffering from long sinus pauses requiring cardiac pacemaker insertion. Patients with CCHS are at risk for pulmonary hypertension and cor pulmonale secondary to chronic hypoxia. Diaphragmatic pacing has been beneficial in some patients with CCHS. In this article, we review concomitant cardiac abnormalities and the occurrence of bradyarrhythmias in patients with CCHS.

Authors+Show Affiliations

Movahed MR
Department of Medicine, Division of Cardiology, University of California, Irvine, USA. mmovahed@uci.edu
Jalili M
No affiliation info available
Kiciman N
No affiliation info available

MeSH

Arrhythmias, CardiacCardiac Pacing, ArtificialCardiovascular AbnormalitiesClinical Trials as TopicHumansPractice Guidelines as TopicPractice Patterns, Physicians'Sleep Apnea, Central

Pub Type(s)

Journal Article
Review

Language

eng

PubMed ID

16359292

Citation

Movahed, Mohammad-Reza, et al. "Cardiovascular Abnormalities and Arrhythmias in Patients With Ondine's Curse (congenital Central Hypoventilation) Syndrome." Pacing and Clinical Electrophysiology : PACE, vol. 28, no. 11, 2005, pp. 1226-30.
Movahed MR, Jalili M, Kiciman N. Cardiovascular abnormalities and arrhythmias in patients with Ondine's curse (congenital central hypoventilation) syndrome. Pacing Clin Electrophysiol. 2005;28(11):1226-30.
Movahed, M. R., Jalili, M., & Kiciman, N. (2005). Cardiovascular abnormalities and arrhythmias in patients with Ondine's curse (congenital central hypoventilation) syndrome. Pacing and Clinical Electrophysiology : PACE, 28(11), 1226-30.
Movahed MR, Jalili M, Kiciman N. Cardiovascular Abnormalities and Arrhythmias in Patients With Ondine's Curse (congenital Central Hypoventilation) Syndrome. Pacing Clin Electrophysiol. 2005;28(11):1226-30. PubMed PMID: 16359292.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Cardiovascular abnormalities and arrhythmias in patients with Ondine's curse (congenital central hypoventilation) syndrome. AU - Movahed,Mohammad-Reza, AU - Jalili,Mehrdad, AU - Kiciman,Nafiz, PY - 2005/12/20/pubmed PY - 2006/2/10/medline PY - 2005/12/20/entrez SP - 1226 EP - 30 JF - Pacing and clinical electrophysiology : PACE JO - Pacing Clin Electrophysiol VL - 28 IS - 11 N2 - Patients with congenital central hypoventilation syndrome (CCHS) (Ondine's curse syndrome) have impaired autonomic control of ventilation with intact voluntary control of respiration. Autonomic dysfunction and cardiac abnormalities are common in CCHS. Bradyarrhythmias are life-threatening and often require pacemaker insertion. We presented a case of a patient with CCHS suffering from long sinus pauses requiring cardiac pacemaker insertion. Patients with CCHS are at risk for pulmonary hypertension and cor pulmonale secondary to chronic hypoxia. Diaphragmatic pacing has been beneficial in some patients with CCHS. In this article, we review concomitant cardiac abnormalities and the occurrence of bradyarrhythmias in patients with CCHS. SN - 0147-8389 UR - https://www.unboundmedicine.com/medline/citation/16359292/Cardiovascular_abnormalities_and_arrhythmias_in_patients_with_Ondine's_curse__congenital_central_hypoventilation__syndrome_ DB - PRIME DP - Unbound Medicine ER -