Tags

Type your tag names separated by a space and hit enter

Scoliosis in a child with Chiari I malformation and the absence of syringomyelia: case report and a review of the literature.
Childs Nerv Syst. 2006 Oct; 22(10):1351-4.CN

Abstract

BACKGROUND

Scoliosis is a common finding in children with Chiari I malformation and syringomyelia. The development of scoliosis associated with a Chiari malformation typically has been ascribed to the presence of syringomyelia. Decompression of the hindbrain hernia will often alleviate the syringomyelia and, in many cases, stabilize or reverse the scoliosis.

CASE REPORT

We report a child with Chiari I malformation and scoliosis who presented with Valsalva-induced headache/neck pain. MRI revealed no syringomyelia or hydrocephalus. Radiographs revealed that her scoliotic curvature was approximately 13 degrees and was a single levoscoliotic curve. This patient underwent a posterior fossa decompression with duraplasty for her Valsalva-induced pain. Postoperatively, she had resolution of her pain and there has been no progression of her scoliosis at 3 years follow-up.

PROGNOSIS

Intriguingly, and scattered throughout the medical literature, many have noted cases of scoliosis in patients with only a Chiari I malformation and no syringomyelia. Moreover, experimental studies have induced scoliosis in animals after compression of the dorsal columns. After a review of the medical literature regarding a potential cause and effect of herniated hindbrain-induced scoliosis in the absence of syringomyelia, this association although rare, does seem plausible.

Authors+Show Affiliations

Department of Cell Biology, University of Alabama at Birmingham, Birmingham, AL, USA. rstubbs@uab.eduNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article
Review

Language

eng

PubMed ID

16532361

Citation

Tubbs, R Shane, et al. "Scoliosis in a Child With Chiari I Malformation and the Absence of Syringomyelia: Case Report and a Review of the Literature." Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery, vol. 22, no. 10, 2006, pp. 1351-4.
Tubbs RS, Doyle S, Conklin M, et al. Scoliosis in a child with Chiari I malformation and the absence of syringomyelia: case report and a review of the literature. Childs Nerv Syst. 2006;22(10):1351-4.
Tubbs, R. S., Doyle, S., Conklin, M., & Oakes, W. J. (2006). Scoliosis in a child with Chiari I malformation and the absence of syringomyelia: case report and a review of the literature. Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery, 22(10), 1351-4.
Tubbs RS, et al. Scoliosis in a Child With Chiari I Malformation and the Absence of Syringomyelia: Case Report and a Review of the Literature. Childs Nerv Syst. 2006;22(10):1351-4. PubMed PMID: 16532361.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Scoliosis in a child with Chiari I malformation and the absence of syringomyelia: case report and a review of the literature. AU - Tubbs,R Shane, AU - Doyle,Scott, AU - Conklin,Michael, AU - Oakes,W Jerry, Y1 - 2006/03/11/ PY - 2005/10/24/received PY - 2006/3/15/pubmed PY - 2007/1/27/medline PY - 2006/3/15/entrez SP - 1351 EP - 4 JF - Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery JO - Childs Nerv Syst VL - 22 IS - 10 N2 - BACKGROUND: Scoliosis is a common finding in children with Chiari I malformation and syringomyelia. The development of scoliosis associated with a Chiari malformation typically has been ascribed to the presence of syringomyelia. Decompression of the hindbrain hernia will often alleviate the syringomyelia and, in many cases, stabilize or reverse the scoliosis. CASE REPORT: We report a child with Chiari I malformation and scoliosis who presented with Valsalva-induced headache/neck pain. MRI revealed no syringomyelia or hydrocephalus. Radiographs revealed that her scoliotic curvature was approximately 13 degrees and was a single levoscoliotic curve. This patient underwent a posterior fossa decompression with duraplasty for her Valsalva-induced pain. Postoperatively, she had resolution of her pain and there has been no progression of her scoliosis at 3 years follow-up. PROGNOSIS: Intriguingly, and scattered throughout the medical literature, many have noted cases of scoliosis in patients with only a Chiari I malformation and no syringomyelia. Moreover, experimental studies have induced scoliosis in animals after compression of the dorsal columns. After a review of the medical literature regarding a potential cause and effect of herniated hindbrain-induced scoliosis in the absence of syringomyelia, this association although rare, does seem plausible. SN - 0256-7040 UR - https://www.unboundmedicine.com/medline/citation/16532361/Scoliosis_in_a_child_with_Chiari_I_malformation_and_the_absence_of_syringomyelia:_case_report_and_a_review_of_the_literature_ L2 - https://doi.org/10.1007/s00381-006-0079-6 DB - PRIME DP - Unbound Medicine ER -