Tags

Type your tag names separated by a space and hit enter

Mucocutaneous bullous amyloidosis with an unusual mixed protein composition of amyloid deposits.
Br J Dermatol. 2006 Apr; 154(4):751-4.BJ

Abstract

We describe a case of fatal systemic amyloidosis presenting with mucocutaneous bullous lesions in a patient with IgA kappa monoclonal gammopathy. The amyloid plaques were composed of an unusual mixture of immunoglobulin kappa light chain and amyloid A proteins. Whereas oesophageal and oropharyngeal blisters are known to occur in several types of bullous dermatoses, to our knowledge this is the first report of oesophagopharyngeal blisters complicating bullous amyloidosis.

Authors+Show Affiliations

Department of Pathology, The Johns Hopkins Medical Institutions, Baltimore, MD 21287, USA. nrekhtm1@jhmi.eduNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

16536823

Citation

Rekhtman, N, et al. "Mucocutaneous Bullous Amyloidosis With an Unusual Mixed Protein Composition of Amyloid Deposits." The British Journal of Dermatology, vol. 154, no. 4, 2006, pp. 751-4.
Rekhtman N, Hash KS, Moresi JM. Mucocutaneous bullous amyloidosis with an unusual mixed protein composition of amyloid deposits. Br J Dermatol. 2006;154(4):751-4.
Rekhtman, N., Hash, K. S., & Moresi, J. M. (2006). Mucocutaneous bullous amyloidosis with an unusual mixed protein composition of amyloid deposits. The British Journal of Dermatology, 154(4), 751-4.
Rekhtman N, Hash KS, Moresi JM. Mucocutaneous Bullous Amyloidosis With an Unusual Mixed Protein Composition of Amyloid Deposits. Br J Dermatol. 2006;154(4):751-4. PubMed PMID: 16536823.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Mucocutaneous bullous amyloidosis with an unusual mixed protein composition of amyloid deposits. AU - Rekhtman,N, AU - Hash,K S, AU - Moresi,J M, PY - 2006/3/16/pubmed PY - 2006/8/10/medline PY - 2006/3/16/entrez SP - 751 EP - 4 JF - The British journal of dermatology JO - Br. J. Dermatol. VL - 154 IS - 4 N2 - We describe a case of fatal systemic amyloidosis presenting with mucocutaneous bullous lesions in a patient with IgA kappa monoclonal gammopathy. The amyloid plaques were composed of an unusual mixture of immunoglobulin kappa light chain and amyloid A proteins. Whereas oesophageal and oropharyngeal blisters are known to occur in several types of bullous dermatoses, to our knowledge this is the first report of oesophagopharyngeal blisters complicating bullous amyloidosis. SN - 0007-0963 UR - https://www.unboundmedicine.com/medline/citation/16536823/Mucocutaneous_bullous_amyloidosis_with_an_unusual_mixed_protein_composition_of_amyloid_deposits_ L2 - https://doi.org/10.1111/j.1365-2133.2005.07063.x DB - PRIME DP - Unbound Medicine ER -