Tags

Type your tag names separated by a space and hit enter

SACRAL syndrome: spinal dysraphism, anogenital, cutaneous, renal and urologic anomalies, associated with an angioma of lumbosacral localization.
Dermatology. 2007; 214(1):40-5.D

Abstract

BACKGROUND

Publications concerning perineal infantile hemangiomas are scarce, and comprise no large series.

OBJECTIVE

Studying clinical features of hemangiomas of the perineal area, complications and associated malformations.

METHODS

Retrospective analysis of all hemangiomas localized in the perineal area, encountered at the Children's Hospital in Bordeaux from 1994.

RESULTS

Of 49 perineal hemangiomas (34 girls, 15 boys), 5 patients had accompanying malformation, mainly lipomyelomeningocele with tethered cord. The superficial hemangiomas were more represented in males and presented sooner than the nodular counterpart. The average rate of ulceration was 73%, ulcerations developed earlier in the superficial forms than their nodular counterparts (2 vs. 4 months).

CONCLUSION

Superficial perineal hemangiomas are more often complicated by ulceration, and are associated with developmental anomalies. As a counterpart for the PHACE syndrome in facial hemangioma, we propose the acronym SACRAL for perineal hemangiomas: Spinal dysraphism, Anogenital anomalies, Cutaneous anomalies, Renal and urologic anomalies, associated with Angioma of Lumbosacral localization.

Links

Publisher Full Text

Authors+Show Affiliations

Stockman A
Pediatric Dermatology Unit, Hôpital Pellegrin-Enfants, Bordeaux, France.
Boralevi F
No affiliation info available
Taïeb A
No affiliation info available
Léauté-Labrèze C
No affiliation info available

MeSH

Anal CanalDiagnosis, DifferentialFemaleFranceHemangiomaHumansIncidenceInfantInfant, NewbornLumbosacral PlexusMalePerineumRetrospective StudiesSex DistributionSkin AbnormalitiesSpinal DysraphismSyndromeUrogenital Abnormalities

Pub Type(s)

Journal Article

Language

eng

PubMed ID

17191046

Citation

Stockman, Annelies, et al. "SACRAL Syndrome: Spinal Dysraphism, Anogenital, Cutaneous, Renal and Urologic Anomalies, Associated With an Angioma of Lumbosacral Localization." Dermatology (Basel, Switzerland), vol. 214, no. 1, 2007, pp. 40-5.
Stockman A, Boralevi F, Taïeb A, et al. SACRAL syndrome: spinal dysraphism, anogenital, cutaneous, renal and urologic anomalies, associated with an angioma of lumbosacral localization. Dermatology. 2007;214(1):40-5.
Stockman, A., Boralevi, F., Taïeb, A., & Léauté-Labrèze, C. (2007). SACRAL syndrome: spinal dysraphism, anogenital, cutaneous, renal and urologic anomalies, associated with an angioma of lumbosacral localization. Dermatology (Basel, Switzerland), 214(1), 40-5.
Stockman A, et al. SACRAL Syndrome: Spinal Dysraphism, Anogenital, Cutaneous, Renal and Urologic Anomalies, Associated With an Angioma of Lumbosacral Localization. Dermatology. 2007;214(1):40-5. PubMed PMID: 17191046.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - SACRAL syndrome: spinal dysraphism, anogenital, cutaneous, renal and urologic anomalies, associated with an angioma of lumbosacral localization. AU - Stockman,Annelies, AU - Boralevi,F, AU - Taïeb,Alain, AU - Léauté-Labrèze,Christine, PY - 2006/03/23/received PY - 2006/06/23/accepted PY - 2006/12/28/pubmed PY - 2007/2/21/medline PY - 2006/12/28/entrez SP - 40 EP - 5 JF - Dermatology (Basel, Switzerland) JO - Dermatology VL - 214 IS - 1 N2 - BACKGROUND: Publications concerning perineal infantile hemangiomas are scarce, and comprise no large series. OBJECTIVE: Studying clinical features of hemangiomas of the perineal area, complications and associated malformations. METHODS: Retrospective analysis of all hemangiomas localized in the perineal area, encountered at the Children's Hospital in Bordeaux from 1994. RESULTS: Of 49 perineal hemangiomas (34 girls, 15 boys), 5 patients had accompanying malformation, mainly lipomyelomeningocele with tethered cord. The superficial hemangiomas were more represented in males and presented sooner than the nodular counterpart. The average rate of ulceration was 73%, ulcerations developed earlier in the superficial forms than their nodular counterparts (2 vs. 4 months). CONCLUSION: Superficial perineal hemangiomas are more often complicated by ulceration, and are associated with developmental anomalies. As a counterpart for the PHACE syndrome in facial hemangioma, we propose the acronym SACRAL for perineal hemangiomas: Spinal dysraphism, Anogenital anomalies, Cutaneous anomalies, Renal and urologic anomalies, associated with Angioma of Lumbosacral localization. SN - 1018-8665 UR - https://www.unboundmedicine.com/medline/citation/17191046/SACRAL_syndrome:_spinal_dysraphism_anogenital_cutaneous_renal_and_urologic_anomalies_associated_with_an_angioma_of_lumbosacral_localization_ L2 - https://www.karger.com?DOI=10.1159/000096911 DB - PRIME DP - Unbound Medicine ER -