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Cochlear implantation in children with Jervell, Lange-Nielsen syndrome.
J Laryngol Otol. 2008 Mar; 122(3):314-7.JL

Abstract

Jervell, Lange-Nielsen syndrome is a condition that causes profound hearing loss and disruption of the normal cardiac rhythm. This disorder is a form of long QT syndrome, a cardiac disorder that causes the cardiac muscle to take longer than usual to recharge between beats. A retrospective case study was performed to document cochlear implantation in three profoundly deaf children (two of them siblings) with Jervell, Lange-Nielsen syndrome. We discuss diagnosis and management of this syndrome and also the long-term performance of cochlear implantation in these Iranian patients, referring especially to the role of the ENT specialist in diagnosis and treatment. The collected data show that cochlear implantation can be relatively safely performed in patients with Jervell, Lange-Nielsen syndrome and that these children received significant benefit from cochlear implantation.

Authors+Show Affiliations

Head and Neck Surgery Department, Iran University of Medical Sciences, Tehran, Iran.No affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

17498328

Citation

Daneshi, A, et al. "Cochlear Implantation in Children With Jervell, Lange-Nielsen Syndrome." The Journal of Laryngology and Otology, vol. 122, no. 3, 2008, pp. 314-7.
Daneshi A, Ghassemi MM, Talee M, et al. Cochlear implantation in children with Jervell, Lange-Nielsen syndrome. J Laryngol Otol. 2008;122(3):314-7.
Daneshi, A., Ghassemi, M. M., Talee, M., & Hassanzadeh, S. (2008). Cochlear implantation in children with Jervell, Lange-Nielsen syndrome. The Journal of Laryngology and Otology, 122(3), 314-7.
Daneshi A, et al. Cochlear Implantation in Children With Jervell, Lange-Nielsen Syndrome. J Laryngol Otol. 2008;122(3):314-7. PubMed PMID: 17498328.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Cochlear implantation in children with Jervell, Lange-Nielsen syndrome. AU - Daneshi,A, AU - Ghassemi,M M, AU - Talee,M, AU - Hassanzadeh,S, Y1 - 2007/05/14/ PY - 2007/5/15/pubmed PY - 2008/6/20/medline PY - 2007/5/15/entrez SP - 314 EP - 7 JF - The Journal of laryngology and otology JO - J Laryngol Otol VL - 122 IS - 3 N2 - Jervell, Lange-Nielsen syndrome is a condition that causes profound hearing loss and disruption of the normal cardiac rhythm. This disorder is a form of long QT syndrome, a cardiac disorder that causes the cardiac muscle to take longer than usual to recharge between beats. A retrospective case study was performed to document cochlear implantation in three profoundly deaf children (two of them siblings) with Jervell, Lange-Nielsen syndrome. We discuss diagnosis and management of this syndrome and also the long-term performance of cochlear implantation in these Iranian patients, referring especially to the role of the ENT specialist in diagnosis and treatment. The collected data show that cochlear implantation can be relatively safely performed in patients with Jervell, Lange-Nielsen syndrome and that these children received significant benefit from cochlear implantation. SN - 1748-5460 UR - https://www.unboundmedicine.com/medline/citation/17498328/Cochlear_implantation_in_children_with_Jervell_Lange_Nielsen_syndrome_ L2 - https://www.cambridge.org/core/product/identifier/S0022215107007712/type/journal_article DB - PRIME DP - Unbound Medicine ER -