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[Compliance of the diet restricted with leucine, isoleucine and valine in maple syrup urine disease (MSUD) children].
Rocz Panstw Zakl Hig. 2007; 58(1):95-101.RP

Abstract

The aim of this study was to evaluate the compliance of the diet with limited branched-chain amino acids (BCAA) content in long-term observation of patients with maple syrup urine disease (MSUD). The study group consisted of 7 children at age of 1.5-18 years. Nutrition evaluation was based on current diet records from 3-4 days, every 3-4 months. Energy and nutrition values of proposed daily products lists and diet records was compared with adequate references and recommendations. Energy and content of most of the nutrients in proposed daily products lists were in agreement with RDI except calcium. Diet analysis at MSUD children revealed insufficient contents of: iron, zinc, copper, vitamin B1, B2, niacin and vitamin C (often below 90% RDI).

Authors+Show Affiliations

Poradnia Zywieniowa, Klinika Pediatrii Instytut Pomnik-Centrum Zdrowia Dziecka, 04-730 Warszawa. kowalikagnieszka@op.plNo affiliation info availableNo affiliation info available

Pub Type(s)

Journal Article

Language

pol

PubMed ID

17711097

Citation

Kowalik, Agnieszka, et al. "[Compliance of the Diet Restricted With Leucine, Isoleucine and Valine in Maple Syrup Urine Disease (MSUD) Children]." Roczniki Panstwowego Zakladu Higieny, vol. 58, no. 1, 2007, pp. 95-101.
Kowalik A, Narojek L, Sykut-Cegielska J. [Compliance of the diet restricted with leucine, isoleucine and valine in maple syrup urine disease (MSUD) children]. Rocz Panstw Zakl Hig. 2007;58(1):95-101.
Kowalik, A., Narojek, L., & Sykut-Cegielska, J. (2007). [Compliance of the diet restricted with leucine, isoleucine and valine in maple syrup urine disease (MSUD) children]. Roczniki Panstwowego Zakladu Higieny, 58(1), 95-101.
Kowalik A, Narojek L, Sykut-Cegielska J. [Compliance of the Diet Restricted With Leucine, Isoleucine and Valine in Maple Syrup Urine Disease (MSUD) Children]. Rocz Panstw Zakl Hig. 2007;58(1):95-101. PubMed PMID: 17711097.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - [Compliance of the diet restricted with leucine, isoleucine and valine in maple syrup urine disease (MSUD) children]. AU - Kowalik,Agnieszka, AU - Narojek,Lucyna, AU - Sykut-Cegielska,Jolanta, PY - 2007/8/23/pubmed PY - 2008/1/11/medline PY - 2007/8/23/entrez SP - 95 EP - 101 JF - Roczniki Panstwowego Zakladu Higieny JO - Rocz Panstw Zakl Hig VL - 58 IS - 1 N2 - The aim of this study was to evaluate the compliance of the diet with limited branched-chain amino acids (BCAA) content in long-term observation of patients with maple syrup urine disease (MSUD). The study group consisted of 7 children at age of 1.5-18 years. Nutrition evaluation was based on current diet records from 3-4 days, every 3-4 months. Energy and nutrition values of proposed daily products lists and diet records was compared with adequate references and recommendations. Energy and content of most of the nutrients in proposed daily products lists were in agreement with RDI except calcium. Diet analysis at MSUD children revealed insufficient contents of: iron, zinc, copper, vitamin B1, B2, niacin and vitamin C (often below 90% RDI). SN - 0035-7715 UR - https://www.unboundmedicine.com/medline/citation/17711097/[Compliance_of_the_diet_restricted_with_leucine_isoleucine_and_valine_in_maple_syrup_urine_disease__MSUD__children]_ DB - PRIME DP - Unbound Medicine ER -