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[Acute respiratory failure as the sol inaugural sign of Arnold-Chiari malformation. Two cases].
Rev Pneumol Clin. 2007 Oct; 63(5 Pt 1):319-22.RP

Abstract

Arnold-Chiari malformation is an occipitocervical malformation where the cerebellar amygdales descend below the occipital foramen. Acute respiratory failure is an exceptional inaugural sign. We report two cases disclosed by alveolar hypoventilation associated with type I Arnold-Chiari malformation. The two patients age 51 and 52 years had an uneventful past history and presented with hypercapnic encephalopathy with acute respiratory failure requiring ventilatory assistance. Respiratory function tests, helicoidal thoracic computed tomographic angiography, electromyogram, cardiac echography, and thyroid and immunological tests were normal. Blood gases and polysomnography were in favor of central hypoventilation without sleep apnea. Magnetic resonance imaging demonstrated type I Arnold-Chiari malformation. The course was complicated by recurrent respiratory failure in both patients. Surgical decompression performed for the first patient provided no improvement. This patient died two months after surgery subsequent to aspiration pneumonia. The second patient was treated with continuous positive pressure noninvasive ventilatory assistance and had a good outcome at 25 months. These two cases illustrate the absence of any neurological sign, acute respiratory failure being the only sign of Arnold-Chiari malformation.

Authors+Show Affiliations

Service de Pneumologie, Pavillon C, Hôpital de Pneumo-Phtisiologie Abderrahman-Mami, 2080 L'Ariana/Tunis, Tunisia.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
English Abstract
Journal Article

Language

fre

PubMed ID

18166935

Citation

Chaouch, N, et al. "[Acute Respiratory Failure as the Sol Inaugural Sign of Arnold-Chiari Malformation. Two Cases]." Revue De Pneumologie Clinique, vol. 63, no. 5 Pt 1, 2007, pp. 319-22.
Chaouch N, Meraï S, Cheikh Rouhou S, et al. [Acute respiratory failure as the sol inaugural sign of Arnold-Chiari malformation. Two cases]. Rev Pneumol Clin. 2007;63(5 Pt 1):319-22.
Chaouch, N., Meraï, S., Cheikh Rouhou, S., Ben Romdhane, K., Ben Mrad, S., Besbes, M., & Tritar, F. (2007). [Acute respiratory failure as the sol inaugural sign of Arnold-Chiari malformation. Two cases]. Revue De Pneumologie Clinique, 63(5 Pt 1), 319-22.
Chaouch N, et al. [Acute Respiratory Failure as the Sol Inaugural Sign of Arnold-Chiari Malformation. Two Cases]. Rev Pneumol Clin. 2007;63(5 Pt 1):319-22. PubMed PMID: 18166935.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - [Acute respiratory failure as the sol inaugural sign of Arnold-Chiari malformation. Two cases]. AU - Chaouch,N, AU - Meraï,S, AU - Cheikh Rouhou,S, AU - Ben Romdhane,K, AU - Ben Mrad,S, AU - Besbes,M, AU - Tritar,F, PY - 2008/1/2/pubmed PY - 2008/2/19/medline PY - 2008/1/2/entrez SP - 319 EP - 22 JF - Revue de pneumologie clinique JO - Rev Pneumol Clin VL - 63 IS - 5 Pt 1 N2 - Arnold-Chiari malformation is an occipitocervical malformation where the cerebellar amygdales descend below the occipital foramen. Acute respiratory failure is an exceptional inaugural sign. We report two cases disclosed by alveolar hypoventilation associated with type I Arnold-Chiari malformation. The two patients age 51 and 52 years had an uneventful past history and presented with hypercapnic encephalopathy with acute respiratory failure requiring ventilatory assistance. Respiratory function tests, helicoidal thoracic computed tomographic angiography, electromyogram, cardiac echography, and thyroid and immunological tests were normal. Blood gases and polysomnography were in favor of central hypoventilation without sleep apnea. Magnetic resonance imaging demonstrated type I Arnold-Chiari malformation. The course was complicated by recurrent respiratory failure in both patients. Surgical decompression performed for the first patient provided no improvement. This patient died two months after surgery subsequent to aspiration pneumonia. The second patient was treated with continuous positive pressure noninvasive ventilatory assistance and had a good outcome at 25 months. These two cases illustrate the absence of any neurological sign, acute respiratory failure being the only sign of Arnold-Chiari malformation. SN - 0761-8417 UR - https://www.unboundmedicine.com/medline/citation/18166935/[Acute_respiratory_failure_as_the_sol_inaugural_sign_of_Arnold_Chiari_malformation__Two_cases]_ L2 - https://linkinghub.elsevier.com/retrieve/pii/MDOI-RPC-10-2007-63-5-0761-8417-101019-200520004 DB - PRIME DP - Unbound Medicine ER -