Tags

Type your tag names separated by a space and hit enter

[Combination of complete atrioventricular septal defect and tetralogy of Fallot: surgical management and its results].
Turk Kardiyol Dern Ars. 2008 Oct; 36(7):461-6.TK

Abstract

OBJECTIVES

Complete atrioventricular septal defect (AVSD) with tetralogy of Fallot (TOF) is a rare congenital heart anomaly. We evaluated surgical results of total repair in patients with TOF and AVSD.

STUDY DESIGN

Seven patients (5 girls, 2 boys; age range 2.5 to 14 years) underwent total repair for AVSD and TOF. Three patients had Down syndrome. Three patients had previous systemic-to-pulmonary shunt operations. Accompanying anomalies were left superior vena cava (n=2), left atrial isomerism (n=1), muscular VSD (n=1), and double outlet right ventricle (n=1). Preoperative diagnoses were based on echocardiographic examinations. The two-patch technique was used for surgical repair. Reconstruction of the right ventricular outflow tract was performed using transannular and infundibular patches in four and three patients, respectively. The follow-up period ranged from six months to nine years (mean 3.4+/-2.9 years).

RESULTS

No mortality occurred throughout the follow-up period. Two patients had prolonged hospitalization (>1 month) due to pulmonary infection and sepsis. At the latest follow-up, functional capacity was NYHA class I in five patients, and class II in two patients. Final echocardiographic examinations showed mild left atrioventricular (AV) valve insufficiency in five patients, and mild (n=3) or moderate (n=1) right AV valve insufficiency. Two patients had mild residual pulmonary stenosis, and three patients with a transannular patch had free pulmonary insufficiency. All the patients had proper right and left ventricular functions and all were in sinus rhythm.

CONCLUSION

With a proper surgical strategy and technique, AVSD and TOF can be corrected successfully. Long-term follow-up is necessary for AV valve dysfunction and pulmonary insufficiency.

Authors+Show Affiliations

Department of Cardiovascular Surgery, Acibadem Bakirköy Hospital, Istanbul, Turkey.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

English Abstract
Journal Article

Language

tur

PubMed ID

19155660

Citation

Sarioğlu, Tayyar, et al. "[Combination of Complete Atrioventricular Septal Defect and Tetralogy of Fallot: Surgical Management and Its Results]." Turk Kardiyoloji Dernegi Arsivi : Turk Kardiyoloji Derneginin Yayin Organidir, vol. 36, no. 7, 2008, pp. 461-6.
Sarioğlu T, Erek E, Yalçinbaş YK, et al. [Combination of complete atrioventricular septal defect and tetralogy of Fallot: surgical management and its results]. Turk Kardiyol Dern Ars. 2008;36(7):461-6.
Sarioğlu, T., Erek, E., Yalçinbaş, Y. K., Türkekul, Y., Saygili, A., Sarioğlu, A., & Ulukol, A. (2008). [Combination of complete atrioventricular septal defect and tetralogy of Fallot: surgical management and its results]. Turk Kardiyoloji Dernegi Arsivi : Turk Kardiyoloji Derneginin Yayin Organidir, 36(7), 461-6.
Sarioğlu T, et al. [Combination of Complete Atrioventricular Septal Defect and Tetralogy of Fallot: Surgical Management and Its Results]. Turk Kardiyol Dern Ars. 2008;36(7):461-6. PubMed PMID: 19155660.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - [Combination of complete atrioventricular septal defect and tetralogy of Fallot: surgical management and its results]. AU - Sarioğlu,Tayyar, AU - Erek,Ersin, AU - Yalçinbaş,Yusuf Kenan, AU - Türkekul,Yasemin, AU - Saygili,Arda, AU - Sarioğlu,Ayşe, AU - Ulukol,Ayşe, PY - 2009/1/22/entrez PY - 2009/1/22/pubmed PY - 2009/5/27/medline SP - 461 EP - 6 JF - Turk Kardiyoloji Dernegi arsivi : Turk Kardiyoloji Derneginin yayin organidir JO - Turk Kardiyol Dern Ars VL - 36 IS - 7 N2 - OBJECTIVES: Complete atrioventricular septal defect (AVSD) with tetralogy of Fallot (TOF) is a rare congenital heart anomaly. We evaluated surgical results of total repair in patients with TOF and AVSD. STUDY DESIGN: Seven patients (5 girls, 2 boys; age range 2.5 to 14 years) underwent total repair for AVSD and TOF. Three patients had Down syndrome. Three patients had previous systemic-to-pulmonary shunt operations. Accompanying anomalies were left superior vena cava (n=2), left atrial isomerism (n=1), muscular VSD (n=1), and double outlet right ventricle (n=1). Preoperative diagnoses were based on echocardiographic examinations. The two-patch technique was used for surgical repair. Reconstruction of the right ventricular outflow tract was performed using transannular and infundibular patches in four and three patients, respectively. The follow-up period ranged from six months to nine years (mean 3.4+/-2.9 years). RESULTS: No mortality occurred throughout the follow-up period. Two patients had prolonged hospitalization (>1 month) due to pulmonary infection and sepsis. At the latest follow-up, functional capacity was NYHA class I in five patients, and class II in two patients. Final echocardiographic examinations showed mild left atrioventricular (AV) valve insufficiency in five patients, and mild (n=3) or moderate (n=1) right AV valve insufficiency. Two patients had mild residual pulmonary stenosis, and three patients with a transannular patch had free pulmonary insufficiency. All the patients had proper right and left ventricular functions and all were in sinus rhythm. CONCLUSION: With a proper surgical strategy and technique, AVSD and TOF can be corrected successfully. Long-term follow-up is necessary for AV valve dysfunction and pulmonary insufficiency. SN - 1016-5169 UR - https://www.unboundmedicine.com/medline/citation/19155660/[Combination_of_complete_atrioventricular_septal_defect_and_tetralogy_of_Fallot:_surgical_management_and_its_results]_ L2 - https://www.journalagent.com/pubmed/linkout.asp?ISSN=1016-5169&PMID=19155660 DB - PRIME DP - Unbound Medicine ER -