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Single-stage total endoscopic resection of a plexiform neurofibroma of the maxillary sinus in a child with type 1 neurofibromatosis.
Int J Pediatr Otorhinolaryngol. 2010 Apr; 74(4):426-9.IJ

Abstract

Plexiform neurofibromas are peripheral nerve sheath tumors associated with neurofibromatosis type 1. The maxillary sinus is an extremely rare location of the plexiform neurofibroma and only two adult cases have been previously reported. We report the first case of plexiform neurofibroma of the maxillary sinus occurring in a child with neurofibromatosis type 1. This unusual location presents a management challenge considering the infiltrative nature and the potential malignant degeneration of this type of tumor. MRI is highly valuable to diagnose and plan the surgical approach of the plexiform neurofibroma of the maxillary sinus. Due to the location of the tumor and the patient's age, conservative surgery is highly recommended. We performed an endoscopic total en-bloc resection of the tumor with no recurrence after nine months of follow-up.

Authors+Show Affiliations

Department of Otolaryngology-Head and Neck Surgery, University of Miami, Miller School of Medicine, Miami, FL, USA.No affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

20074816

Citation

Hachem, Ralph N Abi, et al. "Single-stage Total Endoscopic Resection of a Plexiform Neurofibroma of the Maxillary Sinus in a Child With Type 1 Neurofibromatosis." International Journal of Pediatric Otorhinolaryngology, vol. 74, no. 4, 2010, pp. 426-9.
Hachem RN, Bared A, Zeitouni J, et al. Single-stage total endoscopic resection of a plexiform neurofibroma of the maxillary sinus in a child with type 1 neurofibromatosis. Int J Pediatr Otorhinolaryngol. 2010;74(4):426-9.
Hachem, R. N., Bared, A., Zeitouni, J., & Younis, R. T. (2010). Single-stage total endoscopic resection of a plexiform neurofibroma of the maxillary sinus in a child with type 1 neurofibromatosis. International Journal of Pediatric Otorhinolaryngology, 74(4), 426-9. https://doi.org/10.1016/j.ijporl.2009.12.012
Hachem RN, et al. Single-stage Total Endoscopic Resection of a Plexiform Neurofibroma of the Maxillary Sinus in a Child With Type 1 Neurofibromatosis. Int J Pediatr Otorhinolaryngol. 2010;74(4):426-9. PubMed PMID: 20074816.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Single-stage total endoscopic resection of a plexiform neurofibroma of the maxillary sinus in a child with type 1 neurofibromatosis. AU - Hachem,Ralph N Abi, AU - Bared,Anthony, AU - Zeitouni,Joseph, AU - Younis,Ramzi T, Y1 - 2010/01/13/ PY - 2009/09/11/received PY - 2009/12/16/revised PY - 2009/12/16/accepted PY - 2010/1/16/entrez PY - 2010/1/16/pubmed PY - 2010/6/11/medline SP - 426 EP - 9 JF - International journal of pediatric otorhinolaryngology JO - Int J Pediatr Otorhinolaryngol VL - 74 IS - 4 N2 - Plexiform neurofibromas are peripheral nerve sheath tumors associated with neurofibromatosis type 1. The maxillary sinus is an extremely rare location of the plexiform neurofibroma and only two adult cases have been previously reported. We report the first case of plexiform neurofibroma of the maxillary sinus occurring in a child with neurofibromatosis type 1. This unusual location presents a management challenge considering the infiltrative nature and the potential malignant degeneration of this type of tumor. MRI is highly valuable to diagnose and plan the surgical approach of the plexiform neurofibroma of the maxillary sinus. Due to the location of the tumor and the patient's age, conservative surgery is highly recommended. We performed an endoscopic total en-bloc resection of the tumor with no recurrence after nine months of follow-up. SN - 1872-8464 UR - https://www.unboundmedicine.com/medline/citation/20074816/Single_stage_total_endoscopic_resection_of_a_plexiform_neurofibroma_of_the_maxillary_sinus_in_a_child_with_type_1_neurofibromatosis_ L2 - https://linkinghub.elsevier.com/retrieve/pii/S0165-5876(09)00679-X DB - PRIME DP - Unbound Medicine ER -