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Primary localized cutaneous amyloidosis intermingled with papulopustular lesions in a patient with Behçet's disease.
Rheumatol Int. 2012 Nov; 32(11):3651-3.RI

Abstract

Primary localized cutaneous amyloidosis (PLCA) sometimes shows overlapping with collagen vascular diseases; however, association with Behçet's disease (BD) is rare. We herein report a case of PLCA developing intermingled with papulopustular lesions associated with BD. A 57-year-old woman visited our hospital, complaining of recalcitrant multiple oral aphthae. Further detailed physical examination revealed folliculitis-like small pustules with surrounding erythema on the upper back. Also, she stated past histories of genital ulcers 10 years ago and erythema nodosum on the lower legs 4 years ago. A biopsy specimen from the pustular lesion on the back showed neutrophilic abscess in the epidermis with a number of perivascular inflammatory cells in the upper dermis. Congo-red and Dylon stain revealed amyloid deposition in the papillary dermis. Although association of systemic amyloidosis with BD is occasionally found in the literature, co-occurrence of cutaneous amyloidosis and papulopustular lesions of BD is extremely rare.

Authors+Show Affiliations

Department of Dermatology, Fukushima Medical University, Fukushima 960-1295, Japan. toyamade@fmu.ac.jpNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

20473498

Citation

Yamamoto, Toshiyuki, and Yasuhiro Suzuki. "Primary Localized Cutaneous Amyloidosis Intermingled With Papulopustular Lesions in a Patient With Behçet's Disease." Rheumatology International, vol. 32, no. 11, 2012, pp. 3651-3.
Yamamoto T, Suzuki Y. Primary localized cutaneous amyloidosis intermingled with papulopustular lesions in a patient with Behçet's disease. Rheumatol Int. 2012;32(11):3651-3.
Yamamoto, T., & Suzuki, Y. (2012). Primary localized cutaneous amyloidosis intermingled with papulopustular lesions in a patient with Behçet's disease. Rheumatology International, 32(11), 3651-3. https://doi.org/10.1007/s00296-010-1513-3
Yamamoto T, Suzuki Y. Primary Localized Cutaneous Amyloidosis Intermingled With Papulopustular Lesions in a Patient With Behçet's Disease. Rheumatol Int. 2012;32(11):3651-3. PubMed PMID: 20473498.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Primary localized cutaneous amyloidosis intermingled with papulopustular lesions in a patient with Behçet's disease. AU - Yamamoto,Toshiyuki, AU - Suzuki,Yasuhiro, Y1 - 2010/05/15/ PY - 2010/01/19/received PY - 2010/04/27/accepted PY - 2010/5/18/entrez PY - 2010/5/18/pubmed PY - 2013/5/18/medline SP - 3651 EP - 3 JF - Rheumatology international JO - Rheumatol. Int. VL - 32 IS - 11 N2 - Primary localized cutaneous amyloidosis (PLCA) sometimes shows overlapping with collagen vascular diseases; however, association with Behçet's disease (BD) is rare. We herein report a case of PLCA developing intermingled with papulopustular lesions associated with BD. A 57-year-old woman visited our hospital, complaining of recalcitrant multiple oral aphthae. Further detailed physical examination revealed folliculitis-like small pustules with surrounding erythema on the upper back. Also, she stated past histories of genital ulcers 10 years ago and erythema nodosum on the lower legs 4 years ago. A biopsy specimen from the pustular lesion on the back showed neutrophilic abscess in the epidermis with a number of perivascular inflammatory cells in the upper dermis. Congo-red and Dylon stain revealed amyloid deposition in the papillary dermis. Although association of systemic amyloidosis with BD is occasionally found in the literature, co-occurrence of cutaneous amyloidosis and papulopustular lesions of BD is extremely rare. SN - 1437-160X UR - https://www.unboundmedicine.com/medline/citation/20473498/Primary_localized_cutaneous_amyloidosis_intermingled_with_papulopustular_lesions_in_a_patient_with_Behçet's_disease_ L2 - https://dx.doi.org/10.1007/s00296-010-1513-3 DB - PRIME DP - Unbound Medicine ER -