Tags

Type your tag names separated by a space and hit enter

Giant occipital meningocele in an 8-year-old child with Dandy-Walker malformation.
Childs Nerv Syst. 2011 Jan; 27(1):167-74.CN

Abstract

INTRODUCTION

The possibility of an association between Dandy-Walker malformation and occipital meningocele is well-known. However, just an overall number of about 40 cases have been previously reported. Giant occipital meningocele has been described only in three newborns. Incidence, pathology, clinical presentation, and proper management of this association are still poorly defined.

REPORT OF THE CASE

An 8-year-old boy with Dandy-Walker malformation and giant (25 cm in diameter) occipital meningocele is presented. This boy was born without any apparent occipital mass and harbored no other significant malformations including hydrocephalus. On admission, he was neurologically intact and the giant occipital mass presented partially calcified cyst walls. Treatment consisted of the excision of the occipital malformation, cranioplasty, and cysto-peritoneal shunt. Outcome was excellent.

CONCLUSIONS

To the best of our knowledge, among the few reported patients with Dandy-Walker malformation associated to occipital meningocele, this is the oldest one and the one with the largest occipital meningocele; he is unique with calcified walls of the occipital meningocele and the only one who survived the repair of the giant malformation. In Dandy-Walker malformation, occipital meningocele may develop and grow regardless of hydrocephalus. Giant size may be reached and the cyst may become calcified. Surgical repair may warrant favorable outcome.

Authors+Show Affiliations

Department of Neurosurgery, Niguarda Ca'Granda Hospital, Piazza Ospedale Maggiore 3, Milan, Italy. giuseppe.talamonti@ospedaleniguarda.itNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

20490510

Citation

Talamonti, Giuseppe, et al. "Giant Occipital Meningocele in an 8-year-old Child With Dandy-Walker Malformation." Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery, vol. 27, no. 1, 2011, pp. 167-74.
Talamonti G, Picano M, Debernardi A, et al. Giant occipital meningocele in an 8-year-old child with Dandy-Walker malformation. Childs Nerv Syst. 2011;27(1):167-74.
Talamonti, G., Picano, M., Debernardi, A., Bolzon, M., Teruzzi, M., & D'Aliberti, G. (2011). Giant occipital meningocele in an 8-year-old child with Dandy-Walker malformation. Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery, 27(1), 167-74. https://doi.org/10.1007/s00381-010-1154-6
Talamonti G, et al. Giant Occipital Meningocele in an 8-year-old Child With Dandy-Walker Malformation. Childs Nerv Syst. 2011;27(1):167-74. PubMed PMID: 20490510.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Giant occipital meningocele in an 8-year-old child with Dandy-Walker malformation. AU - Talamonti,Giuseppe, AU - Picano,Marco, AU - Debernardi,Alberto, AU - Bolzon,Moreno, AU - Teruzzi,Mario, AU - D'Aliberti,Giuseppe, Y1 - 2010/05/19/ PY - 2010/03/27/received PY - 2010/04/08/accepted PY - 2010/5/22/entrez PY - 2010/5/22/pubmed PY - 2011/4/29/medline SP - 167 EP - 74 JF - Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery JO - Childs Nerv Syst VL - 27 IS - 1 N2 - INTRODUCTION: The possibility of an association between Dandy-Walker malformation and occipital meningocele is well-known. However, just an overall number of about 40 cases have been previously reported. Giant occipital meningocele has been described only in three newborns. Incidence, pathology, clinical presentation, and proper management of this association are still poorly defined. REPORT OF THE CASE: An 8-year-old boy with Dandy-Walker malformation and giant (25 cm in diameter) occipital meningocele is presented. This boy was born without any apparent occipital mass and harbored no other significant malformations including hydrocephalus. On admission, he was neurologically intact and the giant occipital mass presented partially calcified cyst walls. Treatment consisted of the excision of the occipital malformation, cranioplasty, and cysto-peritoneal shunt. Outcome was excellent. CONCLUSIONS: To the best of our knowledge, among the few reported patients with Dandy-Walker malformation associated to occipital meningocele, this is the oldest one and the one with the largest occipital meningocele; he is unique with calcified walls of the occipital meningocele and the only one who survived the repair of the giant malformation. In Dandy-Walker malformation, occipital meningocele may develop and grow regardless of hydrocephalus. Giant size may be reached and the cyst may become calcified. Surgical repair may warrant favorable outcome. SN - 1433-0350 UR - https://www.unboundmedicine.com/medline/citation/20490510/Giant_occipital_meningocele_in_an_8_year_old_child_with_Dandy_Walker_malformation_ L2 - https://doi.org/10.1007/s00381-010-1154-6 DB - PRIME DP - Unbound Medicine ER -