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Diastematomyelia and tumor in adults: report of two cases and literature review.
Spine (Phila Pa 1976). 2010 Nov 15; 35(24):E1438-43.S

Abstract

STUDY DESIGN

Case report and review of the literature.

OBJECTIVE

To report on 2 rare cases of association of diastematomyelia with dysembryogenetic tumors and revision of the literature.

SUMMARY OF BACKGROUND DATA

Diastematomyelia is an occult spinal diastrophism pathologically characterized by a clefting of the spinal cord with/without its overlying structures. It is often associated with vertebral bony abnormalities, cutaneous lesions, myelomeningocele, hydrocephalus, hydromyelia, Chiari syndrome or Klippel-Feil syndrome. The association of diastematomyelia with dysembryogenetic spinal tumors in adults is extremely rare. Only 13 cases were detected in a literature review since 1951. We report on our experience with 2 new cases.

METHODS

An 87-year-old man and a 38-year-old woman presented to our department with incomplete cauda equina syndrome. Both patients underwent complete preoperative imaging. Complete surgical removal of the tumor was performed. Details of these were compared with the ones encountered in literature.

RESULTS

Both patients presented complete recovery in the follow-up. From the review of 15 adults described in literature including the present cases, the age ranged between 11 and 87 proving an open rage of onset of symptoms.

CONCLUSION

The results of surgery were unclear in literature. In our experience, radical surgery was feasible and good clinical results were obtained.

Authors+Show Affiliations

Department of Neurosurgery, University of Florence, Florence, Italy.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article
Review

Language

eng

PubMed ID

21030887

Citation

Conti, Piero, et al. "Diastematomyelia and Tumor in Adults: Report of Two Cases and Literature Review." Spine, vol. 35, no. 24, 2010, pp. E1438-43.
Conti P, Tenenbaum R, Capozza M, et al. Diastematomyelia and tumor in adults: report of two cases and literature review. Spine. 2010;35(24):E1438-43.
Conti, P., Tenenbaum, R., Capozza, M., Mouchaty, H., & Conti, R. (2010). Diastematomyelia and tumor in adults: report of two cases and literature review. Spine, 35(24), E1438-43. https://doi.org/10.1097/BRS.0b013e3181ebc4a4
Conti P, et al. Diastematomyelia and Tumor in Adults: Report of Two Cases and Literature Review. Spine. 2010 Nov 15;35(24):E1438-43. PubMed PMID: 21030887.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Diastematomyelia and tumor in adults: report of two cases and literature review. AU - Conti,Piero, AU - Tenenbaum,Ron, AU - Capozza,Matteo, AU - Mouchaty,Homere, AU - Conti,Renato, PY - 2010/10/30/entrez PY - 2010/10/30/pubmed PY - 2011/2/26/medline SP - E1438 EP - 43 JF - Spine JO - Spine VL - 35 IS - 24 N2 - STUDY DESIGN: Case report and review of the literature. OBJECTIVE: To report on 2 rare cases of association of diastematomyelia with dysembryogenetic tumors and revision of the literature. SUMMARY OF BACKGROUND DATA: Diastematomyelia is an occult spinal diastrophism pathologically characterized by a clefting of the spinal cord with/without its overlying structures. It is often associated with vertebral bony abnormalities, cutaneous lesions, myelomeningocele, hydrocephalus, hydromyelia, Chiari syndrome or Klippel-Feil syndrome. The association of diastematomyelia with dysembryogenetic spinal tumors in adults is extremely rare. Only 13 cases were detected in a literature review since 1951. We report on our experience with 2 new cases. METHODS: An 87-year-old man and a 38-year-old woman presented to our department with incomplete cauda equina syndrome. Both patients underwent complete preoperative imaging. Complete surgical removal of the tumor was performed. Details of these were compared with the ones encountered in literature. RESULTS: Both patients presented complete recovery in the follow-up. From the review of 15 adults described in literature including the present cases, the age ranged between 11 and 87 proving an open rage of onset of symptoms. CONCLUSION: The results of surgery were unclear in literature. In our experience, radical surgery was feasible and good clinical results were obtained. SN - 1528-1159 UR - https://www.unboundmedicine.com/medline/citation/21030887/Diastematomyelia_and_tumor_in_adults:_report_of_two_cases_and_literature_review_ L2 - http://dx.doi.org/10.1097/BRS.0b013e3181ebc4a4 DB - PRIME DP - Unbound Medicine ER -