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Hydrocephalus in Dandy-Walker malformation.
Childs Nerv Syst. 2011 Oct; 27(10):1665-81.CN

Abstract

INTRODUCTION

Even if the first description of Dandy-Walker dates back 1887, difficulty in the establishment of correct diagnosis, especially concerning differential diagnosis with other types of posterior fossa CSF collection, still persists. Further confusion is added by the inclusion, in some classification, of different malformations with different prognosis and therapeutic strategy under the same label of "Dandy-Walker".

METHODS

An extensive literature review concerning embryologic, etiologic, pathogenetic, clinical and neuroradiological aspects has been performed. Therapeutic options, prognosis and intellectual outcome are also reviewed.

CONCLUSION

The correct interpretation of the modern neuroradiologic techniques, including CSF flow MR imaging, may help in identifying a "real" Dandy-Walker malformation. Among therapeutical strategies, single shunting (ventriculo-peritoneal or cyst-peritoneal shunts) appears effective in the control of both ventricle and cyst size. Endoscopic third ventriculostomy may be considered an acceptable alternative, especially in older children, with the aim to reduce the shunt-related problems. Prognosis and intellectual outcome mostly depend on the presence of associated malformations, the degree of vermian malformation and the adequate control of hydrocephalus.

Authors+Show Affiliations

Department of Pediatric Neurosurgery, Santobono Children's Hospital, Via Mario Fiore n. 6, 80129 Naples, Italy.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Journal Article
Review

Language

eng

PubMed ID

21928031

Citation

Spennato, Pietro, et al. "Hydrocephalus in Dandy-Walker Malformation." Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery, vol. 27, no. 10, 2011, pp. 1665-81.
Spennato P, Mirone G, Nastro A, et al. Hydrocephalus in Dandy-Walker malformation. Childs Nerv Syst. 2011;27(10):1665-81.
Spennato, P., Mirone, G., Nastro, A., Buonocore, M. C., Ruggiero, C., Trischitta, V., Aliberti, F., & Cinalli, G. (2011). Hydrocephalus in Dandy-Walker malformation. Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery, 27(10), 1665-81. https://doi.org/10.1007/s00381-011-1544-4
Spennato P, et al. Hydrocephalus in Dandy-Walker Malformation. Childs Nerv Syst. 2011;27(10):1665-81. PubMed PMID: 21928031.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Hydrocephalus in Dandy-Walker malformation. AU - Spennato,Pietro, AU - Mirone,Giuseppe, AU - Nastro,Anna, AU - Buonocore,Maria Consiglio, AU - Ruggiero,Claudio, AU - Trischitta,Vincenzo, AU - Aliberti,Ferdinando, AU - Cinalli,Giuseppe, Y1 - 2011/09/17/ PY - 2011/07/25/received PY - 2011/07/26/accepted PY - 2011/9/20/entrez PY - 2011/9/20/pubmed PY - 2012/1/25/medline SP - 1665 EP - 81 JF - Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery JO - Childs Nerv Syst VL - 27 IS - 10 N2 - INTRODUCTION: Even if the first description of Dandy-Walker dates back 1887, difficulty in the establishment of correct diagnosis, especially concerning differential diagnosis with other types of posterior fossa CSF collection, still persists. Further confusion is added by the inclusion, in some classification, of different malformations with different prognosis and therapeutic strategy under the same label of "Dandy-Walker". METHODS: An extensive literature review concerning embryologic, etiologic, pathogenetic, clinical and neuroradiological aspects has been performed. Therapeutic options, prognosis and intellectual outcome are also reviewed. CONCLUSION: The correct interpretation of the modern neuroradiologic techniques, including CSF flow MR imaging, may help in identifying a "real" Dandy-Walker malformation. Among therapeutical strategies, single shunting (ventriculo-peritoneal or cyst-peritoneal shunts) appears effective in the control of both ventricle and cyst size. Endoscopic third ventriculostomy may be considered an acceptable alternative, especially in older children, with the aim to reduce the shunt-related problems. Prognosis and intellectual outcome mostly depend on the presence of associated malformations, the degree of vermian malformation and the adequate control of hydrocephalus. SN - 1433-0350 UR - https://www.unboundmedicine.com/medline/citation/21928031/Hydrocephalus_in_Dandy_Walker_malformation_ L2 - https://doi.org/10.1007/s00381-011-1544-4 DB - PRIME DP - Unbound Medicine ER -