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Recurrent bilateral branch retinal artery occlusion with hearing loss and encephalopathy: the first case report of Susac syndrome in Korea.
J Korean Med Sci 2011; 26(11):1518-21JK

Abstract

We report the first case of Susac syndrome in Koreans, in a 23-yr-old female patient who presented with sudden visual loss and associated neurological symptoms. Ophthalmic examination and fluorescein angiography showed multiple areas of branch retinal artery occlusion, which tended to recur in both eyes. Magnetic resonance imaging showed dot-like, diffusion-restricted lesions in the corpus callosum and left fornix, and audiometry showed low-frequency sensory hearing loss, compatible with Susac syndrome. She received immunosuppressive therapy with oral steroid and azathioprine. Three months later all the symptoms disappeared but obstructive vasculitis have been relapsing. This patient demonstrated the entire clinical triad of Susac syndrome, which tends to occur in young females. Although this disorder has rarely been reported in Asian populations, a high index of suspicion is warranted for early diagnosis and timely treatment.

Authors+Show Affiliations

Department of Ophthalmology, Asan Medical Center, University of Ulsan, College of Medicine, Seoul, Korea.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

22065912

Citation

Joe, Soo Geun, et al. "Recurrent Bilateral Branch Retinal Artery Occlusion With Hearing Loss and Encephalopathy: the First Case Report of Susac Syndrome in Korea." Journal of Korean Medical Science, vol. 26, no. 11, 2011, pp. 1518-21.
Joe SG, Kim JG, Kwon SU, et al. Recurrent bilateral branch retinal artery occlusion with hearing loss and encephalopathy: the first case report of Susac syndrome in Korea. J Korean Med Sci. 2011;26(11):1518-21.
Joe, S. G., Kim, J. G., Kwon, S. U., Lee, C. W., Lim, H. W., & Yoon, Y. H. (2011). Recurrent bilateral branch retinal artery occlusion with hearing loss and encephalopathy: the first case report of Susac syndrome in Korea. Journal of Korean Medical Science, 26(11), pp. 1518-21. doi:10.3346/jkms.2011.26.11.1518.
Joe SG, et al. Recurrent Bilateral Branch Retinal Artery Occlusion With Hearing Loss and Encephalopathy: the First Case Report of Susac Syndrome in Korea. J Korean Med Sci. 2011;26(11):1518-21. PubMed PMID: 22065912.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Recurrent bilateral branch retinal artery occlusion with hearing loss and encephalopathy: the first case report of Susac syndrome in Korea. AU - Joe,Soo Geun, AU - Kim,June-Gone, AU - Kwon,Sun Uck, AU - Lee,Choong Wook, AU - Lim,Hyun Woo, AU - Yoon,Young Hee, Y1 - 2011/10/27/ PY - 2011/07/26/received PY - 2011/09/21/accepted PY - 2011/11/9/entrez PY - 2011/11/9/pubmed PY - 2012/5/23/medline KW - Branch Retinal Artery Occlusion KW - Encephalopathy KW - Hearing Loss KW - Korean KW - Susac Syndrome SP - 1518 EP - 21 JF - Journal of Korean medical science JO - J. Korean Med. Sci. VL - 26 IS - 11 N2 - We report the first case of Susac syndrome in Koreans, in a 23-yr-old female patient who presented with sudden visual loss and associated neurological symptoms. Ophthalmic examination and fluorescein angiography showed multiple areas of branch retinal artery occlusion, which tended to recur in both eyes. Magnetic resonance imaging showed dot-like, diffusion-restricted lesions in the corpus callosum and left fornix, and audiometry showed low-frequency sensory hearing loss, compatible with Susac syndrome. She received immunosuppressive therapy with oral steroid and azathioprine. Three months later all the symptoms disappeared but obstructive vasculitis have been relapsing. This patient demonstrated the entire clinical triad of Susac syndrome, which tends to occur in young females. Although this disorder has rarely been reported in Asian populations, a high index of suspicion is warranted for early diagnosis and timely treatment. SN - 1598-6357 UR - https://www.unboundmedicine.com/medline/citation/22065912/Recurrent_bilateral_branch_retinal_artery_occlusion_with_hearing_loss_and_encephalopathy:_the_first_case_report_of_Susac_syndrome_in_Korea_ L2 - https://jkms.org/DOIx.php?id=10.3346/jkms.2011.26.11.1518 DB - PRIME DP - Unbound Medicine ER -