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Intramedullary spinal cord primitive neuroectodermal tumor presenting with hydrocephalus.
J Child Neurol. 2013 Feb; 28(2):246-50.JC

Abstract

Spinal primitive neuroectodermal tumors are exceedingly rare. Herewith, we present the first case of an intramedullary spinal cord tumor associated with hydrocephalus in a 2-month-old boy that presented with left hemiparesis. The patient had been diagnosed on prenatal ultrasound with enlarged ventricular system. At his current admission, a brain magnetic resonance imaging (MRI) revealed hydrocephalus and an intramedullary lesion extending from the second cervical to the first thoracic vertebrae. Dissemination of the tumor was revealed intracranially and in the spinal canal. After a ventriculoperitoneal shunt placement a radical resection of the tumor was performed, however some small tumor remnants could not be safely removed. Postoperative there was no neurologic deterioration. The tumor was diagnosed as a central nervous system primitive neuroectodermal tumor (World Health Organization grade IV). Spinal intramedullary primitive neuroectodermal tumors are extremely rare. In such rare tumors, multiinstitutional studies are needed for treatment guidelines to be established.

Authors+Show Affiliations

Department of Neurosurgery, Children's Hospital Agia Sofia, Athens, Greece. alexiougrg@yahoo.grNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

22532539

Citation

Alexiou, George A., et al. "Intramedullary Spinal Cord Primitive Neuroectodermal Tumor Presenting With Hydrocephalus." Journal of Child Neurology, vol. 28, no. 2, 2013, pp. 246-50.
Alexiou GA, Siozos G, Stefanaki K, et al. Intramedullary spinal cord primitive neuroectodermal tumor presenting with hydrocephalus. J Child Neurol. 2013;28(2):246-50.
Alexiou, G. A., Siozos, G., Stefanaki, K., Moschovi, M., & Prodromou, N. (2013). Intramedullary spinal cord primitive neuroectodermal tumor presenting with hydrocephalus. Journal of Child Neurology, 28(2), 246-50. https://doi.org/10.1177/0883073812441061
Alexiou GA, et al. Intramedullary Spinal Cord Primitive Neuroectodermal Tumor Presenting With Hydrocephalus. J Child Neurol. 2013;28(2):246-50. PubMed PMID: 22532539.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Intramedullary spinal cord primitive neuroectodermal tumor presenting with hydrocephalus. AU - Alexiou,George A, AU - Siozos,George, AU - Stefanaki,Kalliopi, AU - Moschovi,Maria, AU - Prodromou,Neofytos, Y1 - 2012/04/24/ PY - 2012/4/26/entrez PY - 2012/4/26/pubmed PY - 2013/8/13/medline SP - 246 EP - 50 JF - Journal of child neurology JO - J. Child Neurol. VL - 28 IS - 2 N2 - Spinal primitive neuroectodermal tumors are exceedingly rare. Herewith, we present the first case of an intramedullary spinal cord tumor associated with hydrocephalus in a 2-month-old boy that presented with left hemiparesis. The patient had been diagnosed on prenatal ultrasound with enlarged ventricular system. At his current admission, a brain magnetic resonance imaging (MRI) revealed hydrocephalus and an intramedullary lesion extending from the second cervical to the first thoracic vertebrae. Dissemination of the tumor was revealed intracranially and in the spinal canal. After a ventriculoperitoneal shunt placement a radical resection of the tumor was performed, however some small tumor remnants could not be safely removed. Postoperative there was no neurologic deterioration. The tumor was diagnosed as a central nervous system primitive neuroectodermal tumor (World Health Organization grade IV). Spinal intramedullary primitive neuroectodermal tumors are extremely rare. In such rare tumors, multiinstitutional studies are needed for treatment guidelines to be established. SN - 1708-8283 UR - https://www.unboundmedicine.com/medline/citation/22532539/Intramedullary_spinal_cord_primitive_neuroectodermal_tumor_presenting_with_hydrocephalus_ L2 - http://journals.sagepub.com/doi/full/10.1177/0883073812441061?url_ver=Z39.88-2003&rfr_id=ori:rid:crossref.org&rfr_dat=cr_pub=pubmed DB - PRIME DP - Unbound Medicine ER -