Tags

Type your tag names separated by a space and hit enter

Tongue reduction for macroglossia in Beckwith Wiedemann syndrome: review and application of new technique.
Int J Oral Maxillofac Surg. 2013 Feb; 42(2):185-91.IJ

Abstract

Beckwith Wiedemann syndrome (BWS) is a rare, congenital overgrowth disorder that is characterized by macroglossia, anterior abdominal wall defects, visceromegaly, gigantism, and neonatal hypoglycaemia. Macroglossia may contribute to anterior open bite malocclusion with prognathism, speech articulation disturbances, drooling and the perception of intellectual disability. It was the purpose of this study to review a series of BWS patients who underwent surgical reduction of the tongue by a modified technique with respect to aesthetic and functional outcomes. Seven BWS patients, age 6 months to 21 months, had a 'stellate/anterior wedge' reduction with an anterior rotation flap and were followed up from 4 months to 9 years postoperatively. Assessment of aesthetics together with tongue morphology and mobility were recorded and a postoperative speech evaluation was performed. Minor contour deformities were present in two patients during function but all parents were satisfied with the results. The speech pathology assessment results indicated positive outcomes for speech, oral structure and function, and feeding for all children assessed. This modified technique allows for an adequate reduction of tongue volume with conservation of motor and sensory function as well as preservation of anatomical contour.

Authors+Show Affiliations

Department of Plastic and Maxillofacial Surgery, Royal Children's Hospital, Melbourne, Australia. aheggie@bigpond.net.auNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Clinical Trial
Journal Article

Language

eng

PubMed ID

23041202

Citation

Heggie, A A C., et al. "Tongue Reduction for Macroglossia in Beckwith Wiedemann Syndrome: Review and Application of New Technique." International Journal of Oral and Maxillofacial Surgery, vol. 42, no. 2, 2013, pp. 185-91.
Heggie AA, Vujcich NJ, Portnof JE, et al. Tongue reduction for macroglossia in Beckwith Wiedemann syndrome: review and application of new technique. Int J Oral Maxillofac Surg. 2013;42(2):185-91.
Heggie, A. A., Vujcich, N. J., Portnof, J. E., & Morgan, A. T. (2013). Tongue reduction for macroglossia in Beckwith Wiedemann syndrome: review and application of new technique. International Journal of Oral and Maxillofacial Surgery, 42(2), 185-91. https://doi.org/10.1016/j.ijom.2012.09.003
Heggie AA, et al. Tongue Reduction for Macroglossia in Beckwith Wiedemann Syndrome: Review and Application of New Technique. Int J Oral Maxillofac Surg. 2013;42(2):185-91. PubMed PMID: 23041202.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Tongue reduction for macroglossia in Beckwith Wiedemann syndrome: review and application of new technique. AU - Heggie,A A C, AU - Vujcich,N J, AU - Portnof,J E, AU - Morgan,A T, Y1 - 2012/10/04/ PY - 2012/04/25/received PY - 2012/07/31/revised PY - 2012/09/05/accepted PY - 2012/10/9/entrez PY - 2012/10/9/pubmed PY - 2013/7/25/medline SP - 185 EP - 91 JF - International journal of oral and maxillofacial surgery JO - Int J Oral Maxillofac Surg VL - 42 IS - 2 N2 - Beckwith Wiedemann syndrome (BWS) is a rare, congenital overgrowth disorder that is characterized by macroglossia, anterior abdominal wall defects, visceromegaly, gigantism, and neonatal hypoglycaemia. Macroglossia may contribute to anterior open bite malocclusion with prognathism, speech articulation disturbances, drooling and the perception of intellectual disability. It was the purpose of this study to review a series of BWS patients who underwent surgical reduction of the tongue by a modified technique with respect to aesthetic and functional outcomes. Seven BWS patients, age 6 months to 21 months, had a 'stellate/anterior wedge' reduction with an anterior rotation flap and were followed up from 4 months to 9 years postoperatively. Assessment of aesthetics together with tongue morphology and mobility were recorded and a postoperative speech evaluation was performed. Minor contour deformities were present in two patients during function but all parents were satisfied with the results. The speech pathology assessment results indicated positive outcomes for speech, oral structure and function, and feeding for all children assessed. This modified technique allows for an adequate reduction of tongue volume with conservation of motor and sensory function as well as preservation of anatomical contour. SN - 1399-0020 UR - https://www.unboundmedicine.com/medline/citation/23041202/Tongue_reduction_for_macroglossia_in_Beckwith_Wiedemann_syndrome:_review_and_application_of_new_technique_ L2 - https://linkinghub.elsevier.com/retrieve/pii/S0901-5027(12)00378-5 DB - PRIME DP - Unbound Medicine ER -