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Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report.
Arq Bras Oftalmol 2013 May-Jun; 76(3):192-4AB

Abstract

We report the case of a 24-year-old man presenting with sudden visual loss in the left eye from a central retinal artery occlusion. An extensive clinical investigation revealed no etiology. Three weeks later, however, the patient developed hearing loss followed by encephalopathy and multiple branch retinal artery occlusions in the right eye. Fluorescein angiography confirmed retinal vascular occlusions with no sign of vasculitis. The neurological examination revealed a diffuse encephalopathy while the MRI scan disclosed several small areas of infarcts in the brain. Bilateral sensorineural hearing loss was confirmed on audiometry. The patient was diagnosed with Susac syndrome and treated with methylprednisolone and cyclophosphamide, resulting in slight improvement and stabilization. This case shows that Susac syndrome may be diagnosed late due to the absence at onset of one or more of the symptoms of the classic triad (encephalopathy, multiple branch retinal artery occlusions and hearing loss). This case also serves to emphasize that Susac syndrome should be considered in the differential diagnosis of central retinal artery occlusion, even in apparently healthy young men.

Authors+Show Affiliations

Department of Neurology, Universidade de São Paulo - USP - São Paulo (SP), Brazil.No affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

23929083

Citation

Apóstolos-Pereira, Samira Luiza dos, et al. "Unilateral Central Retinal Artery Occlusion as the Sole Presenting Sign of Susac Syndrome in a Young Man: Case Report." Arquivos Brasileiros De Oftalmologia, vol. 76, no. 3, 2013, pp. 192-4.
Apóstolos-Pereira SL, Kara-José LB, Marchiori PE, et al. Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report. Arq Bras Oftalmol. 2013;76(3):192-4.
Apóstolos-Pereira, S. L., Kara-José, L. B., Marchiori, P. E., & Monteiro, M. L. (2013). Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report. Arquivos Brasileiros De Oftalmologia, 76(3), pp. 192-4.
Apóstolos-Pereira SL, et al. Unilateral Central Retinal Artery Occlusion as the Sole Presenting Sign of Susac Syndrome in a Young Man: Case Report. Arq Bras Oftalmol. 2013;76(3):192-4. PubMed PMID: 23929083.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report. AU - Apóstolos-Pereira,Samira Luiza dos, AU - Kara-José,Lúcia B Passos, AU - Marchiori,Paulo Euripedes, AU - Monteiro,Mário Luiz Ribeiro, PY - 2013/06/18/received PY - 2013/06/22/accepted PY - 2013/8/10/entrez PY - 2013/8/10/pubmed PY - 2014/3/22/medline SP - 192 EP - 4 JF - Arquivos brasileiros de oftalmologia JO - Arq Bras Oftalmol VL - 76 IS - 3 N2 - We report the case of a 24-year-old man presenting with sudden visual loss in the left eye from a central retinal artery occlusion. An extensive clinical investigation revealed no etiology. Three weeks later, however, the patient developed hearing loss followed by encephalopathy and multiple branch retinal artery occlusions in the right eye. Fluorescein angiography confirmed retinal vascular occlusions with no sign of vasculitis. The neurological examination revealed a diffuse encephalopathy while the MRI scan disclosed several small areas of infarcts in the brain. Bilateral sensorineural hearing loss was confirmed on audiometry. The patient was diagnosed with Susac syndrome and treated with methylprednisolone and cyclophosphamide, resulting in slight improvement and stabilization. This case shows that Susac syndrome may be diagnosed late due to the absence at onset of one or more of the symptoms of the classic triad (encephalopathy, multiple branch retinal artery occlusions and hearing loss). This case also serves to emphasize that Susac syndrome should be considered in the differential diagnosis of central retinal artery occlusion, even in apparently healthy young men. SN - 1678-2925 UR - https://www.unboundmedicine.com/medline/citation/23929083/Unilateral_central_retinal_artery_occlusion_as_the_sole_presenting_sign_of_Susac_syndrome_in_a_young_man:_case_report_ L2 - http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-27492013000300013&lng=en&nrm=iso&tlng=en DB - PRIME DP - Unbound Medicine ER -