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Aggressive giant cystic lymphatic malformation in a newborn.
Turk J Pediatr. 2013 Jul-Aug; 55(4):447-50.TJ

Abstract

Lymphatic malformations are uncommon, benign and congenital malformations of the lymphatic system exhibiting lack of development of communication between the lymphatic and venous circulation. We report the unusual case of rapidly expanding giant lymphatic malformation of the torso, bilateral axillae and left upper extremity of a newborn. As the first-line treatment, aspiration and sclerotherapy with bleomycin were performed. The sclerotherapy failed to cause regression of the mass, and rapid expansion of the malformation necessitated surgery. Partial resection of the mass was performed. Clinical symptoms of respiratory distress resolved in the early postoperative period, and the patient became hemodynamically stable. However, intrathoracic invasion of the mass developed, leading to restriction of thoracic expansion, ending in death. In conclusion, surgical treatment of giant lymphatic malformations remains challenging.

Authors+Show Affiliations

Department of Plastic, Reconstructive and Aesthetic Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey. mertcalis@gmail.com.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

24292043

Citation

Calış, Mert, et al. "Aggressive Giant Cystic Lymphatic Malformation in a Newborn." The Turkish Journal of Pediatrics, vol. 55, no. 4, 2013, pp. 447-50.
Calış M, Konaş E, Takcı Ş, et al. Aggressive giant cystic lymphatic malformation in a newborn. Turk J Pediatr. 2013;55(4):447-50.
Calış, M., Konaş, E., Takcı, Ş., Yurdakök, M., & Tunçbilek, G. (2013). Aggressive giant cystic lymphatic malformation in a newborn. The Turkish Journal of Pediatrics, 55(4), 447-50.
Calış M, et al. Aggressive Giant Cystic Lymphatic Malformation in a Newborn. Turk J Pediatr. 2013 Jul-Aug;55(4):447-50. PubMed PMID: 24292043.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Aggressive giant cystic lymphatic malformation in a newborn. AU - Calış,Mert, AU - Konaş,Ersoy, AU - Takcı,Şahin, AU - Yurdakök,Murat, AU - Tunçbilek,Gökhan, PY - 2013/12/3/entrez PY - 2013/12/3/pubmed PY - 2014/8/6/medline SP - 447 EP - 50 JF - The Turkish journal of pediatrics JO - Turk. J. Pediatr. VL - 55 IS - 4 N2 - Lymphatic malformations are uncommon, benign and congenital malformations of the lymphatic system exhibiting lack of development of communication between the lymphatic and venous circulation. We report the unusual case of rapidly expanding giant lymphatic malformation of the torso, bilateral axillae and left upper extremity of a newborn. As the first-line treatment, aspiration and sclerotherapy with bleomycin were performed. The sclerotherapy failed to cause regression of the mass, and rapid expansion of the malformation necessitated surgery. Partial resection of the mass was performed. Clinical symptoms of respiratory distress resolved in the early postoperative period, and the patient became hemodynamically stable. However, intrathoracic invasion of the mass developed, leading to restriction of thoracic expansion, ending in death. In conclusion, surgical treatment of giant lymphatic malformations remains challenging. SN - 0041-4301 UR - https://www.unboundmedicine.com/medline/citation/24292043/Aggressive_giant_cystic_lymphatic_malformation_in_a_newborn_ L2 - https://medlineplus.gov/headandneckcancer.html DB - PRIME DP - Unbound Medicine ER -