Tags

Type your tag names separated by a space and hit enter

Clinicoradiological correlation of scoliosis in children with Jarcho-Levin and Escobar syndromes: associated "flat bone or wing-like" imaging findings.
Eur J Pediatr. 2014 Oct; 173(10):1377-80.EJ

Abstract

Congenital or early onset scoliosis may be the lead clinical feature in several rare syndromes. In this paper, we present the imaging findings in two children with early onset scoliosis related to the Jarcho-Levin and Escobar syndromes and an osseous plate or wing-like bar extending along the posterior elements of the spine on computed tomography. The clinical phenotypes in these syndromes are variable. A thorough clinical evaluation with imaging correlation is essential. The recognition of underlying spinal anomalies is essential in planning treatment and estimating prognosis. In young children with progressive scoliosis, cross-sectional imaging plays a major role in the diagnostic work-up.

CONCLUSION

Congenital scoliosis requires a comprehensive clinical evaluation and imaging work-up. The presence of an osseous plate or wing-like fusion of posterior elements of the spine may suggest the diagnosis of Jarcho-Levin and Escobar syndromes.

Authors+Show Affiliations

Section of Pediatric Neuroradiology, Division of Pediatric Radiology, The Russell H. Morgan Department of Radiology and Radiological Science, The Johns Hopkins University School of Medicine, Charlotte R. Bloomberg Children's Center, Sheikh Zayed Tower, Room 4174, 1800 Orleans Street, Baltimore, MD, 21287-0842, USA, tbosema1@jhmi.edu.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

24791932

Citation

Bosemani, Thangamadhan, et al. "Clinicoradiological Correlation of Scoliosis in Children With Jarcho-Levin and Escobar Syndromes: Associated "flat Bone or Wing-like" Imaging Findings." European Journal of Pediatrics, vol. 173, no. 10, 2014, pp. 1377-80.
Bosemani T, Poretti A, Benson JE, et al. Clinicoradiological correlation of scoliosis in children with Jarcho-Levin and Escobar syndromes: associated "flat bone or wing-like" imaging findings. Eur J Pediatr. 2014;173(10):1377-80.
Bosemani, T., Poretti, A., Benson, J. E., Meyer-Heim, A., & Huisman, T. A. (2014). Clinicoradiological correlation of scoliosis in children with Jarcho-Levin and Escobar syndromes: associated "flat bone or wing-like" imaging findings. European Journal of Pediatrics, 173(10), 1377-80. https://doi.org/10.1007/s00431-014-2324-4
Bosemani T, et al. Clinicoradiological Correlation of Scoliosis in Children With Jarcho-Levin and Escobar Syndromes: Associated "flat Bone or Wing-like" Imaging Findings. Eur J Pediatr. 2014;173(10):1377-80. PubMed PMID: 24791932.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Clinicoradiological correlation of scoliosis in children with Jarcho-Levin and Escobar syndromes: associated "flat bone or wing-like" imaging findings. AU - Bosemani,Thangamadhan, AU - Poretti,Andrea, AU - Benson,Jane E, AU - Meyer-Heim,Andreas, AU - Huisman,Thierry A G M, Y1 - 2014/05/03/ PY - 2014/02/26/received PY - 2014/04/16/accepted PY - 2014/04/15/revised PY - 2014/5/6/entrez PY - 2014/5/6/pubmed PY - 2015/5/30/medline SP - 1377 EP - 80 JF - European journal of pediatrics JO - Eur J Pediatr VL - 173 IS - 10 N2 - UNLABELLED: Congenital or early onset scoliosis may be the lead clinical feature in several rare syndromes. In this paper, we present the imaging findings in two children with early onset scoliosis related to the Jarcho-Levin and Escobar syndromes and an osseous plate or wing-like bar extending along the posterior elements of the spine on computed tomography. The clinical phenotypes in these syndromes are variable. A thorough clinical evaluation with imaging correlation is essential. The recognition of underlying spinal anomalies is essential in planning treatment and estimating prognosis. In young children with progressive scoliosis, cross-sectional imaging plays a major role in the diagnostic work-up. CONCLUSION: Congenital scoliosis requires a comprehensive clinical evaluation and imaging work-up. The presence of an osseous plate or wing-like fusion of posterior elements of the spine may suggest the diagnosis of Jarcho-Levin and Escobar syndromes. SN - 1432-1076 UR - https://www.unboundmedicine.com/medline/citation/24791932/Clinicoradiological_correlation_of_scoliosis_in_children_with_Jarcho-Levin_and_Escobar_syndromes:_associated_"flat_bone_or_wing-like"_imaging_findings L2 - https://dx.doi.org/10.1007/s00431-014-2324-4 DB - PRIME DP - Unbound Medicine ER -