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Hemorrhagic intramedullary hemangioblastoma of the cervical spinal cord presenting with acute-onset quadriparesis: case report and review of the literature.
J Spinal Cord Med. 2014 Nov; 37(6):791-4.JS

Abstract

CONTEXT

Hemangioblastomas of the spinal cord are uncommon vascular tumors. Patients commonly present with subtle neurologic findings that are thought to represent growth of the lesion over time. Hemorrhage of an intramedullary hemangioblastoma presenting as acute neurologic deficit is an extremely rare occurrence. Although the cervical spine is the most common location for hemangioblastoma of the spinal cord, there have been no previously published cases in the literature of intramedullary hemorrhage from such a lesion.

FINDINGS

A 22-year-old woman with a previously undiagnosed spinal cord hemangioblastoma presented with sudden-onset dense quadriparesis due to intramedullary hemorrhage in the cervical spinal cord. The patient did not have any clinical findings of von-Hippel Lindau disease. Laminoplasty from C5 to T2 and posterior midline myelotomy for resection of the intramedullary tumor with hematoma evacuation were completed without complication.

CONCLUSION

Intramedullary hemangioblastoma of the spinal cord is uncommon, and hemorrhage from a cervical spinal cord lesion has not previously been reported. Symptoms from these usually indolent lesions are commonly associated with tumor growth, edema, or associated syrinx, whereas devastating acute neurologic deficit from hemorrhage is exceedingly rare. Microsurgical resection should be done in cases of symptomatic lesions and considered in isolated symptomatic lesions without the known diagnosis of von Hippel-Lindau disease.

Authors

No affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article
Review

Language

eng

PubMed ID

25029412

Citation

Gluf, Wayne M., and Andrew T. Dailey. "Hemorrhagic Intramedullary Hemangioblastoma of the Cervical Spinal Cord Presenting With Acute-onset Quadriparesis: Case Report and Review of the Literature." The Journal of Spinal Cord Medicine, vol. 37, no. 6, 2014, pp. 791-4.
Gluf WM, Dailey AT. Hemorrhagic intramedullary hemangioblastoma of the cervical spinal cord presenting with acute-onset quadriparesis: case report and review of the literature. J Spinal Cord Med. 2014;37(6):791-4.
Gluf, W. M., & Dailey, A. T. (2014). Hemorrhagic intramedullary hemangioblastoma of the cervical spinal cord presenting with acute-onset quadriparesis: case report and review of the literature. The Journal of Spinal Cord Medicine, 37(6), 791-4. https://doi.org/10.1179/2045772314Y.0000000210
Gluf WM, Dailey AT. Hemorrhagic Intramedullary Hemangioblastoma of the Cervical Spinal Cord Presenting With Acute-onset Quadriparesis: Case Report and Review of the Literature. J Spinal Cord Med. 2014;37(6):791-4. PubMed PMID: 25029412.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Hemorrhagic intramedullary hemangioblastoma of the cervical spinal cord presenting with acute-onset quadriparesis: case report and review of the literature. AU - Gluf,Wayne M, AU - Dailey,Andrew T, Y1 - 2014/07/16/ PY - 2014/7/17/entrez PY - 2014/7/17/pubmed PY - 2015/1/21/medline KW - Cervical vertebrae KW - Hemangioblastoma KW - Hemorrhage KW - Spinal cord neoplasms SP - 791 EP - 4 JF - The journal of spinal cord medicine JO - J Spinal Cord Med VL - 37 IS - 6 N2 - CONTEXT: Hemangioblastomas of the spinal cord are uncommon vascular tumors. Patients commonly present with subtle neurologic findings that are thought to represent growth of the lesion over time. Hemorrhage of an intramedullary hemangioblastoma presenting as acute neurologic deficit is an extremely rare occurrence. Although the cervical spine is the most common location for hemangioblastoma of the spinal cord, there have been no previously published cases in the literature of intramedullary hemorrhage from such a lesion. FINDINGS: A 22-year-old woman with a previously undiagnosed spinal cord hemangioblastoma presented with sudden-onset dense quadriparesis due to intramedullary hemorrhage in the cervical spinal cord. The patient did not have any clinical findings of von-Hippel Lindau disease. Laminoplasty from C5 to T2 and posterior midline myelotomy for resection of the intramedullary tumor with hematoma evacuation were completed without complication. CONCLUSION: Intramedullary hemangioblastoma of the spinal cord is uncommon, and hemorrhage from a cervical spinal cord lesion has not previously been reported. Symptoms from these usually indolent lesions are commonly associated with tumor growth, edema, or associated syrinx, whereas devastating acute neurologic deficit from hemorrhage is exceedingly rare. Microsurgical resection should be done in cases of symptomatic lesions and considered in isolated symptomatic lesions without the known diagnosis of von Hippel-Lindau disease. SN - 1079-0268 UR - https://www.unboundmedicine.com/medline/citation/25029412/Hemorrhagic_intramedullary_hemangioblastoma_of_the_cervical_spinal_cord_presenting_with_acute_onset_quadriparesis:_case_report_and_review_of_the_literature_ L2 - http://www.tandfonline.com/doi/full/10.1179/2045772314Y.0000000210 DB - PRIME DP - Unbound Medicine ER -