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Susac syndrome: diverse clinical findings and treatment.
Arq Bras Oftalmol 2014 May-Jun; 77(3):188-90AB

Abstract

We report a case of a 19-year-old woman presenting bilateral neurosensorial hearing loss, mental abnormalities, and loss of visual field in the left eye. Visual acuity was 20/20 in OD and 20/25 in OS. Patient was examined systemically. Audiometry showed sensorineural hearing loss in both ears. The magnetic resonance imaging (MRI) of brain revealed multiple small lesions in the white matter in both cerebral hemispheres and at the corpus callosum. Fundoscopy showed bilateral normal optic disc and sheathing of the arterioles in the middle periphery of OD. Retinal edema and cotton-wool spots were observed. Fluorescein angiography showed bilateral peripheral occlusive arterial vasculopathy. The patient was diagnosed with Susac syndrome and treated with quetiapine fumarate, flunitrazepam, and prednisone, which resulted in stabile outcome. This case shows that a high index of suspicion leading to early recognition and treatment is important to avoid irreversible damage.

Authors+Show Affiliations

Department of Ophthalmology, Hospital Evangélico, Curitiba, PR, Brazil.Department of Ophthalmology, Universidade Federal de São Paulo, São Paulo, SP, Brazil.Paraná Eye Hospital, Curitiba, PR, Brazil.Paraná Eye Hospital, Curitiba, PR, Brazil.Department of Ophthalmology, Universidade Federal de São Paulo, São Paulo, SP, Brazil.Department of Ophthalmology, Universidade Federal de São Paulo, São Paulo, SP, Brazil.Paraná Eye Hospital, Curitiba, PR, Brazil.Department of Ophthalmology, Universidade Federal de São Paulo, São Paulo, SP, Brazil.

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

25295909

Citation

Bardal, Ricardo Canto, et al. "Susac Syndrome: Diverse Clinical Findings and Treatment." Arquivos Brasileiros De Oftalmologia, vol. 77, no. 3, 2014, pp. 188-90.
Bardal RC, Badaro E, Arana J, et al. Susac syndrome: diverse clinical findings and treatment. Arq Bras Oftalmol. 2014;77(3):188-90.
Bardal, R. C., Badaro, E., Arana, J., Alves, F., Souza, E. C., Bonomo, P. P., ... Maia, M. (2014). Susac syndrome: diverse clinical findings and treatment. Arquivos Brasileiros De Oftalmologia, 77(3), pp. 188-90.
Bardal RC, et al. Susac Syndrome: Diverse Clinical Findings and Treatment. Arq Bras Oftalmol. 2014;77(3):188-90. PubMed PMID: 25295909.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Susac syndrome: diverse clinical findings and treatment. AU - Bardal,Ricardo Canto, AU - Badaro,Emmerson, AU - Arana,Jayme, AU - Alves,Fabio, AU - Souza,Eduardo Cunha de, AU - Bonomo,Pedro Paulo, AU - Portella,Ezequiel, AU - Maia,Mauricio, PY - 2013/12/02/received PY - 2013/12/06/accepted PY - 2014/10/9/entrez PY - 2014/10/9/pubmed PY - 2015/4/14/medline SP - 188 EP - 90 JF - Arquivos brasileiros de oftalmologia JO - Arq Bras Oftalmol VL - 77 IS - 3 N2 - We report a case of a 19-year-old woman presenting bilateral neurosensorial hearing loss, mental abnormalities, and loss of visual field in the left eye. Visual acuity was 20/20 in OD and 20/25 in OS. Patient was examined systemically. Audiometry showed sensorineural hearing loss in both ears. The magnetic resonance imaging (MRI) of brain revealed multiple small lesions in the white matter in both cerebral hemispheres and at the corpus callosum. Fundoscopy showed bilateral normal optic disc and sheathing of the arterioles in the middle periphery of OD. Retinal edema and cotton-wool spots were observed. Fluorescein angiography showed bilateral peripheral occlusive arterial vasculopathy. The patient was diagnosed with Susac syndrome and treated with quetiapine fumarate, flunitrazepam, and prednisone, which resulted in stabile outcome. This case shows that a high index of suspicion leading to early recognition and treatment is important to avoid irreversible damage. SN - 1678-2925 UR - https://www.unboundmedicine.com/medline/citation/25295909/Susac_syndrome:_diverse_clinical_findings_and_treatment_ L2 - http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-27492014000300188&lng=en&nrm=iso&tlng=en DB - PRIME DP - Unbound Medicine ER -