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Spinal Neurenteric Cyst in Association with Klippel-Feil Syndrome: Case Report and Literature Review.
World Neurosurg. 2015 Aug; 84(2):592.e9-14.WN

Abstract

BACKGROUND

Spinal neurenteric cysts, also known as endodermal or enterogenous cysts, are rare epithelium-lined structures of presumed endodermal origin. Congenital vertebral anomalies are frequently seen in patients with neurenteric cysts, most typically anterior spina bifida, butterfly vertebrae, and hemivertebrae. However, few series of intraspinal neurenteric cysts accompanied by Klippel-Feil syndrome have been reported previously.

CASE DESCRIPTION

Our purpose is to present the clinical, radiological, and histological results of a 29-year-old patient with a spinal neurenteric cyst associated with Klippel-Feil syndrome and to review previous reported cases of neurenteric cysts associated with Klippel-Feil syndrome. In our patient, cervical radiography demonstrated C5-T1 vertebral fusion and magnetic resonance imaging revealed a large intradural cystic mass. The cystic lesion was removed successfully, and it was histopathologically diagnosed as a neurenteric cyst.

CONCLUSION

Neurenteric cysts should always be considered in the differential diagnosis of an intraspinal cystic mass seen in the setting of vertebral anomalies.

Authors+Show Affiliations

Department of Neurosurgery, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA; Department of Neurosurgery, Erasmus Medical Center, Rotterdam, The Netherlands. Electronic address: acan@mgh.harvard.edu.Department of Neurosurgery, Erasmus Medical Center, Rotterdam, The Netherlands.Department of Radiology, Erasmus Medical Center, Rotterdam, The Netherlands.Department of Pathology, Erasmus Medical Center, Rotterdam, The Netherlands.Department of Neurosurgery, Erasmus Medical Center, Rotterdam, The Netherlands.

Pub Type(s)

Case Reports
Journal Article
Review

Language

eng

PubMed ID

25790871

Citation

Can, Anil, et al. "Spinal Neurenteric Cyst in Association With Klippel-Feil Syndrome: Case Report and Literature Review." World Neurosurgery, vol. 84, no. 2, 2015, pp. 592.e9-14.
Can A, Dos Santos Rubio EJ, Jasperse B, et al. Spinal Neurenteric Cyst in Association with Klippel-Feil Syndrome: Case Report and Literature Review. World Neurosurg. 2015;84(2):592.e9-14.
Can, A., Dos Santos Rubio, E. J., Jasperse, B., Verdijk, R. M., & Harhangi, B. S. (2015). Spinal Neurenteric Cyst in Association with Klippel-Feil Syndrome: Case Report and Literature Review. World Neurosurgery, 84(2), e9-14. https://doi.org/10.1016/j.wneu.2015.03.015
Can A, et al. Spinal Neurenteric Cyst in Association With Klippel-Feil Syndrome: Case Report and Literature Review. World Neurosurg. 2015;84(2):592.e9-14. PubMed PMID: 25790871.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Spinal Neurenteric Cyst in Association with Klippel-Feil Syndrome: Case Report and Literature Review. AU - Can,Anil, AU - Dos Santos Rubio,Ellianne J, AU - Jasperse,Bas, AU - Verdijk,Robert M, AU - Harhangi,B Sanjay, Y1 - 2015/03/17/ PY - 2015/01/24/received PY - 2015/03/08/revised PY - 2015/03/09/accepted PY - 2015/3/21/entrez PY - 2015/3/21/pubmed PY - 2015/10/29/medline KW - Congenital cyst KW - Endodermal cyst KW - Enterogenous cyst KW - Klippel-Feil anomaly KW - Neurenteric cyst KW - Spinal cyst SP - 592.e9 EP - 14 JF - World neurosurgery JO - World Neurosurg VL - 84 IS - 2 N2 - BACKGROUND: Spinal neurenteric cysts, also known as endodermal or enterogenous cysts, are rare epithelium-lined structures of presumed endodermal origin. Congenital vertebral anomalies are frequently seen in patients with neurenteric cysts, most typically anterior spina bifida, butterfly vertebrae, and hemivertebrae. However, few series of intraspinal neurenteric cysts accompanied by Klippel-Feil syndrome have been reported previously. CASE DESCRIPTION: Our purpose is to present the clinical, radiological, and histological results of a 29-year-old patient with a spinal neurenteric cyst associated with Klippel-Feil syndrome and to review previous reported cases of neurenteric cysts associated with Klippel-Feil syndrome. In our patient, cervical radiography demonstrated C5-T1 vertebral fusion and magnetic resonance imaging revealed a large intradural cystic mass. The cystic lesion was removed successfully, and it was histopathologically diagnosed as a neurenteric cyst. CONCLUSION: Neurenteric cysts should always be considered in the differential diagnosis of an intraspinal cystic mass seen in the setting of vertebral anomalies. SN - 1878-8769 UR - https://www.unboundmedicine.com/medline/citation/25790871/Spinal_Neurenteric_Cyst_in_Association_with_Klippel_Feil_Syndrome:_Case_Report_and_Literature_Review_ L2 - https://linkinghub.elsevier.com/retrieve/pii/S1878-8750(15)00250-8 DB - PRIME DP - Unbound Medicine ER -