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Rapunzel syndrome presenting as jejuno-jejunal intussusception.
Clin J Gastroenterol 2015; 8(4):202-6CJ

Abstract

The term Rapunzel syndrome is used to describe a trichobezoar of the stomach with a long tail of hair extending into the duodenum and small intestine. It is a rare clinical entity, and it is even rarer in these cases that jejuno-jejunal intussusception and resulting intestinal obstruction is a presenting feature. We report one such case, a young female who presented in the emergency department with abdominal pain and bilious vomiting of short duration. Contrast-enhanced CT of the abdomen enabled a diagnosis of a trichobezoar in the stomach extending into the small gut, along with jejuno-jejunal intussusception. On exploration, gastrotomy was performed to remove the gastric trichobezoar, and jejuno-jejunal intussusception was found on three segments in the proximal jejunum, which was resolved upon complete removal of the tail of the bezoar. This case report is unusual, since intussusception is a rare occurrence in Rapunzel syndrome, and this is the first time that it has been diagnosed preoperatively.

Authors+Show Affiliations

Post Graduate Institute of Medical Sciences-Surgery, 2452, Sector I, HUDA Rohtak, Rohtak, 124001, Haryana, India, drsanjay.marwah@gmail.com.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

26108306

Citation

Marwah, Sanjay, et al. "Rapunzel Syndrome Presenting as Jejuno-jejunal Intussusception." Clinical Journal of Gastroenterology, vol. 8, no. 4, 2015, pp. 202-6.
Marwah S, Pandey S, Raj A, et al. Rapunzel syndrome presenting as jejuno-jejunal intussusception. Clin J Gastroenterol. 2015;8(4):202-6.
Marwah, S., Pandey, S., Raj, A., Jangra, M. S., & Sharma, H. (2015). Rapunzel syndrome presenting as jejuno-jejunal intussusception. Clinical Journal of Gastroenterology, 8(4), pp. 202-6. doi:10.1007/s12328-015-0578-7.
Marwah S, et al. Rapunzel Syndrome Presenting as Jejuno-jejunal Intussusception. Clin J Gastroenterol. 2015;8(4):202-6. PubMed PMID: 26108306.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Rapunzel syndrome presenting as jejuno-jejunal intussusception. AU - Marwah,Sanjay, AU - Pandey,Siddharth, AU - Raj,Abhishek, AU - Jangra,Mahavir Singh, AU - Sharma,Himanshu, Y1 - 2015/06/25/ PY - 2015/04/27/received PY - 2015/06/11/accepted PY - 2015/6/26/entrez PY - 2015/6/26/pubmed PY - 2016/5/24/medline SP - 202 EP - 6 JF - Clinical journal of gastroenterology JO - Clin J Gastroenterol VL - 8 IS - 4 N2 - The term Rapunzel syndrome is used to describe a trichobezoar of the stomach with a long tail of hair extending into the duodenum and small intestine. It is a rare clinical entity, and it is even rarer in these cases that jejuno-jejunal intussusception and resulting intestinal obstruction is a presenting feature. We report one such case, a young female who presented in the emergency department with abdominal pain and bilious vomiting of short duration. Contrast-enhanced CT of the abdomen enabled a diagnosis of a trichobezoar in the stomach extending into the small gut, along with jejuno-jejunal intussusception. On exploration, gastrotomy was performed to remove the gastric trichobezoar, and jejuno-jejunal intussusception was found on three segments in the proximal jejunum, which was resolved upon complete removal of the tail of the bezoar. This case report is unusual, since intussusception is a rare occurrence in Rapunzel syndrome, and this is the first time that it has been diagnosed preoperatively. SN - 1865-7265 UR - https://www.unboundmedicine.com/medline/citation/26108306/Rapunzel_syndrome_presenting_as_jejuno_jejunal_intussusception_ L2 - https://dx.doi.org/10.1007/s12328-015-0578-7 DB - PRIME DP - Unbound Medicine ER -