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Suprasellar Primitive Neuroectodermal Tumor in an Adult.
J Neuroophthalmol. 2016 09; 36(3):299-303.JN

Abstract

Primitive neuroectodermal tumors (PNET) of the central nervous system (CNS) are a heterogeneous group of embryonal malignancies that are composed of undifferentiated or poorly differentiated neuroepithelial cells. Supratentorial PNET is the second most common CNS embryonal malignancy in children, but it is rare in adults. We report the case of a 31-year-old woman with bilateral vision loss and a bitemporal hemianopia. Neuroimaging revealed a suprasellar mass, and pathology was consistent with PNET. After surgical debulking of the tumor followed by radiation therapy and chemotherapy, the patient had significant visual recovery and remained stable over 14 months of follow-up.

Authors+Show Affiliations

Department of Ophthalmology (AEBP), Centro Médico Zambrano Hellion-Tec Salud, Monterrey, Mexico; Department of Ophthalmology (KK, AGL), Baylor College of Medicine, Houston, Texas; Department of Ophthalmology, Houston Methodist Hospital, Houston, Texas; Department of Pathology and Genomic Medicine (MLM, AGL), Houston Methodist Hospital, Houston, Texas; Departments of Ophthalmology (AGL), Neurology, and Neurosurgery, Weill Cornell Medical College, Houston, Texas; Department of Ophthalmology (AGL), UTMB Galveston, Texas; The UT M.D. Anderson Cancer Center (AGL), Houston, Texas; and The University of Iowa Hospitals and Clinics (AGL), Iowa City, Iowa.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

26517622

Citation

Espino Barros Palau, Angelina, et al. "Suprasellar Primitive Neuroectodermal Tumor in an Adult." Journal of Neuro-ophthalmology : the Official Journal of the North American Neuro-Ophthalmology Society, vol. 36, no. 3, 2016, pp. 299-303.
Espino Barros Palau A, Khan K, Morgan ML, et al. Suprasellar Primitive Neuroectodermal Tumor in an Adult. J Neuroophthalmol. 2016;36(3):299-303.
Espino Barros Palau, A., Khan, K., Morgan, M. L., Powell, S. Z., & Lee, A. G. (2016). Suprasellar Primitive Neuroectodermal Tumor in an Adult. Journal of Neuro-ophthalmology : the Official Journal of the North American Neuro-Ophthalmology Society, 36(3), 299-303. https://doi.org/10.1097/WNO.0000000000000312
Espino Barros Palau A, et al. Suprasellar Primitive Neuroectodermal Tumor in an Adult. J Neuroophthalmol. 2016;36(3):299-303. PubMed PMID: 26517622.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Suprasellar Primitive Neuroectodermal Tumor in an Adult. AU - Espino Barros Palau,Angelina, AU - Khan,Khurrum, AU - Morgan,Michael L, AU - Powell,Suzanne Z, AU - Lee,Andrew G, PY - 2015/10/31/entrez PY - 2015/10/31/pubmed PY - 2017/9/2/medline SP - 299 EP - 303 JF - Journal of neuro-ophthalmology : the official journal of the North American Neuro-Ophthalmology Society JO - J Neuroophthalmol VL - 36 IS - 3 N2 - Primitive neuroectodermal tumors (PNET) of the central nervous system (CNS) are a heterogeneous group of embryonal malignancies that are composed of undifferentiated or poorly differentiated neuroepithelial cells. Supratentorial PNET is the second most common CNS embryonal malignancy in children, but it is rare in adults. We report the case of a 31-year-old woman with bilateral vision loss and a bitemporal hemianopia. Neuroimaging revealed a suprasellar mass, and pathology was consistent with PNET. After surgical debulking of the tumor followed by radiation therapy and chemotherapy, the patient had significant visual recovery and remained stable over 14 months of follow-up. SN - 1536-5166 UR - https://www.unboundmedicine.com/medline/citation/26517622/Suprasellar_Primitive_Neuroectodermal_Tumor_in_an_Adult_ L2 - http://dx.doi.org/10.1097/WNO.0000000000000312 DB - PRIME DP - Unbound Medicine ER -