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A pediatric case of relapsed pulmonary alveolar proteinosis despite successful whole lung lavage.
Korean J Pediatr. 2017 Jul; 60(7):232-236.KJ

Abstract

Pulmonary alveolar proteinosis (PAP) is a rare disease in children characterized by intra-alveolar accumulation of surfactant proteins, which severely reduces gaseous exchange. Whole lung lavage (WLL) is the preferred technique for the treatment of severe PAP. Herein, we present a pediatric case of PAP treated with WLL. An 11-year-old boy was admitted with the chief complaint of a dry cough lasting 6 months. He developed symptoms of dyspnea on exertion and had difficulty in climbing stairs. He was ultimately diagnosed with PAP through video-assisted thoracoscopic lung biopsy. As first-line of treatment for PAP, he underwent therapeutic WLL for each of his lungs on separate days. After a brief recovery, his symptoms gradually worsened; therefore, he underwent a second WLL. This is the first pediatric case of PAP relapse despite successful WLL in Korea.

Authors+Show Affiliations

Department of Pediatrics, Seoul National University Hospital, Seoul, Korea.Department of Pediatrics, Seoul National University Hospital, Seoul, Korea.Department of Pediatrics, Seoul National University Hospital, Seoul, Korea.Department of Pediatrics, Seoul National University Hospital, Seoul, Korea.Department of Anesthesiology and Pain Medicine, Seoul National University Hospital, Seoul, Korea.Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul, Korea.Department of Internal Medicine and Lung Institute, Seoul National University Hospital, Seoul, Korea.Department of Radiology, Seoul National University Hospital, Seoul, Korea.Department of Radiology, Seoul National University Hospital, Seoul, Korea.Department of Pediatrics, Seoul National University Hospital, Seoul, Korea.

Pub Type(s)

Journal Article

Language

eng

PubMed ID

28861115

Citation

Jin, Seung Young, et al. "A Pediatric Case of Relapsed Pulmonary Alveolar Proteinosis Despite Successful Whole Lung Lavage." Korean Journal of Pediatrics, vol. 60, no. 7, 2017, pp. 232-236.
Jin SY, Yun HR, Choi YJ, et al. A pediatric case of relapsed pulmonary alveolar proteinosis despite successful whole lung lavage. Korean J Pediatr. 2017;60(7):232-236.
Jin, S. Y., Yun, H. R., Choi, Y. J., Park, J. D., Kim, J. T., Kang, C. H., Park, Y. S., Choi, Y. H., Kim, W. S., & Suh, D. I. (2017). A pediatric case of relapsed pulmonary alveolar proteinosis despite successful whole lung lavage. Korean Journal of Pediatrics, 60(7), 232-236. https://doi.org/10.3345/kjp.2017.60.7.232
Jin SY, et al. A Pediatric Case of Relapsed Pulmonary Alveolar Proteinosis Despite Successful Whole Lung Lavage. Korean J Pediatr. 2017;60(7):232-236. PubMed PMID: 28861115.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - A pediatric case of relapsed pulmonary alveolar proteinosis despite successful whole lung lavage. AU - Jin,Seung Young, AU - Yun,Hye Ri, AU - Choi,Yun Jung, AU - Park,Jun Dong, AU - Kim,Jin Tae, AU - Kang,Chang Hyun, AU - Park,Young Sik, AU - Choi,Young Hun, AU - Kim,Woo Sun, AU - Suh,Dong In, Y1 - 2017/07/31/ PY - 2017/02/20/received PY - 2017/05/11/revised PY - 2017/05/17/accepted PY - 2017/9/2/entrez PY - 2017/9/2/pubmed PY - 2017/9/2/medline KW - Child KW - Pulmonary alveolar proteinosis KW - Recurrence KW - Therapeutic irrigation KW - Video-assisted surgery SP - 232 EP - 236 JF - Korean journal of pediatrics JO - Korean J Pediatr VL - 60 IS - 7 N2 - Pulmonary alveolar proteinosis (PAP) is a rare disease in children characterized by intra-alveolar accumulation of surfactant proteins, which severely reduces gaseous exchange. Whole lung lavage (WLL) is the preferred technique for the treatment of severe PAP. Herein, we present a pediatric case of PAP treated with WLL. An 11-year-old boy was admitted with the chief complaint of a dry cough lasting 6 months. He developed symptoms of dyspnea on exertion and had difficulty in climbing stairs. He was ultimately diagnosed with PAP through video-assisted thoracoscopic lung biopsy. As first-line of treatment for PAP, he underwent therapeutic WLL for each of his lungs on separate days. After a brief recovery, his symptoms gradually worsened; therefore, he underwent a second WLL. This is the first pediatric case of PAP relapse despite successful WLL in Korea. SN - 1738-1061 UR - https://www.unboundmedicine.com/medline/citation/28861115/A_pediatric_case_of_relapsed_pulmonary_alveolar_proteinosis_despite_successful_whole_lung_lavage_ L2 - https://kjp.or.kr/journal/view.php?doi=10.3345/kjp.2017.60.7.232 DB - PRIME DP - Unbound Medicine ER -
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