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Rapunzel syndrome (gastric trichobezoar), a rare presentation with generalised oedema: case report and review of the literature.
Paediatr Int Child Health 2019; 39(1):76-78PI

Abstract

Rapunzel syndrome is a rare form of gastric trichobezoar. A 4-year-old girl presented with generalised oedema and an epigastric mass. Her family was of a relatively low socio-economic background. There was microcytic hypochromic anaemia, hypoalbuminaemia and an elevated α1-antitrypsin clearance. Abdominal ultrasound and non-contrast computed tomography demonstrated a heterogeneous mass related to the stomach. Upper gastro-intestinal tract endoscopy failed to remove it. Surgical laparotomy was undertaken through a single anterior gastrotomy incision and a large mass was extracted which was a cast of the duodenum and stomach and had a tail of approximately 60 cm in length which extended to the jejunum. Low socio-economic status, child neglect and pica are risk factors for trichobezoars. Surgical laparotomy is the optimal treatment of large bezoars.

Authors+Show Affiliations

a Department of Paediatrics, Faculty of Medicine , Mansoura University , Mansoura , Egypt.a Department of Paediatrics, Faculty of Medicine , Mansoura University , Mansoura , Egypt.a Department of Paediatrics, Faculty of Medicine , Mansoura University , Mansoura , Egypt.a Department of Paediatrics, Faculty of Medicine , Mansoura University , Mansoura , Egypt.a Department of Paediatrics, Faculty of Medicine , Mansoura University , Mansoura , Egypt.a Department of Paediatrics, Faculty of Medicine , Mansoura University , Mansoura , Egypt.

Pub Type(s)

Case Reports
Journal Article
Review

Language

eng

PubMed ID

29057712

Citation

Nour, Islam, et al. "Rapunzel Syndrome (gastric Trichobezoar), a Rare Presentation With Generalised Oedema: Case Report and Review of the Literature." Paediatrics and International Child Health, vol. 39, no. 1, 2019, pp. 76-78.
Nour I, Abd Alatef M, Megahed A, et al. Rapunzel syndrome (gastric trichobezoar), a rare presentation with generalised oedema: case report and review of the literature. Paediatr Int Child Health. 2019;39(1):76-78.
Nour, I., Abd Alatef, M., Megahed, A., Yahia, S., Wahba, Y., & Shabaan, A. E. (2019). Rapunzel syndrome (gastric trichobezoar), a rare presentation with generalised oedema: case report and review of the literature. Paediatrics and International Child Health, 39(1), pp. 76-78. doi:10.1080/20469047.2017.1389809.
Nour I, et al. Rapunzel Syndrome (gastric Trichobezoar), a Rare Presentation With Generalised Oedema: Case Report and Review of the Literature. Paediatr Int Child Health. 2019;39(1):76-78. PubMed PMID: 29057712.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Rapunzel syndrome (gastric trichobezoar), a rare presentation with generalised oedema: case report and review of the literature. AU - Nour,Islam, AU - Abd Alatef,Mona, AU - Megahed,Ahmed, AU - Yahia,Sohier, AU - Wahba,Yahya, AU - Shabaan,Abd Elazeez, Y1 - 2017/10/23/ PY - 2017/10/24/pubmed PY - 2019/5/7/medline PY - 2017/10/24/entrez KW - Egyptian KW - Oedema KW - Rapunzel syndrome KW - endoscopy KW - epigastric KW - laparotomy KW - trichobezoars SP - 76 EP - 78 JF - Paediatrics and international child health JO - Paediatr Int Child Health VL - 39 IS - 1 N2 - Rapunzel syndrome is a rare form of gastric trichobezoar. A 4-year-old girl presented with generalised oedema and an epigastric mass. Her family was of a relatively low socio-economic background. There was microcytic hypochromic anaemia, hypoalbuminaemia and an elevated α1-antitrypsin clearance. Abdominal ultrasound and non-contrast computed tomography demonstrated a heterogeneous mass related to the stomach. Upper gastro-intestinal tract endoscopy failed to remove it. Surgical laparotomy was undertaken through a single anterior gastrotomy incision and a large mass was extracted which was a cast of the duodenum and stomach and had a tail of approximately 60 cm in length which extended to the jejunum. Low socio-economic status, child neglect and pica are risk factors for trichobezoars. Surgical laparotomy is the optimal treatment of large bezoars. SN - 2046-9055 UR - https://www.unboundmedicine.com/medline/citation/29057712/Rapunzel_syndrome__gastric_trichobezoar__a_rare_presentation_with_generalised_oedema:_case_report_and_review_of_the_literature_ L2 - http://www.tandfonline.com/doi/full/10.1080/20469047.2017.1389809 DB - PRIME DP - Unbound Medicine ER -