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A Rare Initial Presentation of Primary Diffuse Leptomeningeal PNET in a 10-Year-Old-Male.
S D Med. 2017 Dec; 70(12):543-545.SD

Abstract

Primary leptomeningeal primitive neuroectodermal tumors (PNETs) are extremely rare childhood central nervous system malignancies harboring a very poor prognosis. There is no consensus treatment for these tumors to date. We report a case of a 10-year-old male who presented with mental status change, hydrocephalus, intracranial and spinal diffuse leptomeningeal enhancement without a primary mass upon cranial imaging and a negative initial biopsy until five months into his presentation. He responded significantly well to initial chemotherapy and radiotherapy.

Authors+Show Affiliations

Avera Medical Group Pediatrics, Mitchell, South Dakota.Geisinger Medical Center.Geisinger Medical Center.Geisinger Medical Center.Geisinger Medical Center.

Pub Type(s)

Case Reports

Language

eng

PubMed ID

29334442

Citation

Lim, Peter Paul, et al. "A Rare Initial Presentation of Primary Diffuse Leptomeningeal PNET in a 10-Year-Old-Male." South Dakota Medicine : the Journal of the South Dakota State Medical Association, vol. 70, no. 12, 2017, pp. 543-545.
Lim PP, Ramdas J, Miller MA, et al. A Rare Initial Presentation of Primary Diffuse Leptomeningeal PNET in a 10-Year-Old-Male. S D Med. 2017;70(12):543-545.
Lim, P. P., Ramdas, J., Miller, M. A., Schuerch, C., & Wu, G. (2017). A Rare Initial Presentation of Primary Diffuse Leptomeningeal PNET in a 10-Year-Old-Male. South Dakota Medicine : the Journal of the South Dakota State Medical Association, 70(12), 543-545.
Lim PP, et al. A Rare Initial Presentation of Primary Diffuse Leptomeningeal PNET in a 10-Year-Old-Male. S D Med. 2017;70(12):543-545. PubMed PMID: 29334442.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - A Rare Initial Presentation of Primary Diffuse Leptomeningeal PNET in a 10-Year-Old-Male. AU - Lim,Peter Paul, AU - Ramdas,Jagadeesh, AU - Miller,Michal Ann, AU - Schuerch,Conrad, AU - Wu,George, PY - 2018/1/16/entrez PY - 2018/1/16/pubmed PY - 2019/4/27/medline SP - 543 EP - 545 JF - South Dakota medicine : the journal of the South Dakota State Medical Association JO - S D Med VL - 70 IS - 12 N2 - Primary leptomeningeal primitive neuroectodermal tumors (PNETs) are extremely rare childhood central nervous system malignancies harboring a very poor prognosis. There is no consensus treatment for these tumors to date. We report a case of a 10-year-old male who presented with mental status change, hydrocephalus, intracranial and spinal diffuse leptomeningeal enhancement without a primary mass upon cranial imaging and a negative initial biopsy until five months into his presentation. He responded significantly well to initial chemotherapy and radiotherapy. SN - 0038-3317 UR - https://www.unboundmedicine.com/medline/citation/29334442/A_Rare_Initial_Presentation_of_Primary_Diffuse_Leptomeningeal_PNET_in_a_10_Year_Old_Male_ DB - PRIME DP - Unbound Medicine ER -