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Congenital lymphangioma circumscriptum of vulva presenting as multiple giant mass lesions: a case report and literature review.
J Obstet Gynaecol Res. 2018 May; 44(5):978-982.JO

Abstract

A G2L2 33-year-old woman presented to our clinic with large verrucous warty masses in labia major, perinea and the end portion of her spine measuring about 15 × 7, 9 × 7 and 8 × 8 cm, which had been enlarged following puberty and pregnancy. Her right upper and left lower limbs had gross congenital lymphedema. The masses were removed by superficial partial vulvectomy with a qualified margin and repaired without skin graft. Pathology report showed lymphangioma circumscriptum. Several months of follow up revealed normal healing and no recurrence. In conclusion, congenital vulvar lymphangioma, which is a rare disorder, can be highly triggered by hormonal-stimulating situations like puberty and pregnancy. Thus, it is better to visit the affected cases in a timely manner in order to excise these lesions before massive enlargement. In our experience, a superficial partial vulvectomy without skin graft can be a sufficient procedure. Obviously, an appropriate approach during and after surgery would be very important for obtaining a desirable healing.

Authors+Show Affiliations

Department of Gynecology Oncology, Vali-Asr Hospital, Tehran University of Medical Sciences, Tehran, Iran.Department of Obstetrics and Gynecology Oncology, Sabzevar University of Medical Sciences, Sabzevar, Iran.Department of Pathology, Cancer Institute, Imam Khomeini Hospital Complex, Tehran, Iran.

Pub Type(s)

Case Reports

Language

eng

PubMed ID

29484773

Citation

Akhavan, Setareh, et al. "Congenital Lymphangioma Circumscriptum of Vulva Presenting as Multiple Giant Mass Lesions: a Case Report and Literature Review." The Journal of Obstetrics and Gynaecology Research, vol. 44, no. 5, 2018, pp. 978-982.
Akhavan S, Agah J, Nili F. Congenital lymphangioma circumscriptum of vulva presenting as multiple giant mass lesions: a case report and literature review. J Obstet Gynaecol Res. 2018;44(5):978-982.
Akhavan, S., Agah, J., & Nili, F. (2018). Congenital lymphangioma circumscriptum of vulva presenting as multiple giant mass lesions: a case report and literature review. The Journal of Obstetrics and Gynaecology Research, 44(5), 978-982. https://doi.org/10.1111/jog.13609
Akhavan S, Agah J, Nili F. Congenital Lymphangioma Circumscriptum of Vulva Presenting as Multiple Giant Mass Lesions: a Case Report and Literature Review. J Obstet Gynaecol Res. 2018;44(5):978-982. PubMed PMID: 29484773.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Congenital lymphangioma circumscriptum of vulva presenting as multiple giant mass lesions: a case report and literature review. AU - Akhavan,Setareh, AU - Agah,Jila, AU - Nili,Fatemeh, Y1 - 2018/02/27/ PY - 2017/07/18/received PY - 2018/01/07/accepted PY - 2018/2/28/pubmed PY - 2018/10/23/medline PY - 2018/2/28/entrez KW - congenital KW - lymphangioma circumscriptum KW - lymphedema KW - vulva SP - 978 EP - 982 JF - The journal of obstetrics and gynaecology research JO - J. Obstet. Gynaecol. Res. VL - 44 IS - 5 N2 - A G2L2 33-year-old woman presented to our clinic with large verrucous warty masses in labia major, perinea and the end portion of her spine measuring about 15 × 7, 9 × 7 and 8 × 8 cm, which had been enlarged following puberty and pregnancy. Her right upper and left lower limbs had gross congenital lymphedema. The masses were removed by superficial partial vulvectomy with a qualified margin and repaired without skin graft. Pathology report showed lymphangioma circumscriptum. Several months of follow up revealed normal healing and no recurrence. In conclusion, congenital vulvar lymphangioma, which is a rare disorder, can be highly triggered by hormonal-stimulating situations like puberty and pregnancy. Thus, it is better to visit the affected cases in a timely manner in order to excise these lesions before massive enlargement. In our experience, a superficial partial vulvectomy without skin graft can be a sufficient procedure. Obviously, an appropriate approach during and after surgery would be very important for obtaining a desirable healing. SN - 1447-0756 UR - https://www.unboundmedicine.com/medline/citation/29484773/Congenital_lymphangioma_circumscriptum_of_vulva_presenting_as_multiple_giant_mass_lesions:_a_case_report_and_literature_review_ L2 - https://doi.org/10.1111/jog.13609 DB - PRIME DP - Unbound Medicine ER -
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